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Absent right atrioventricular connection with the left atrium connected to a left-sided dominant right ventricle—anatomical and functional aspects in four cases

Published online by Cambridge University Press:  19 August 2008

Munir Ebaid ,
José Fernando Cavalini  and
Vera Demarchi Aiello
Munir Ebaid*
Affiliation:
From the Divisions of Pediatric Cardiology, Heart Institute, São Paulo
José Fernando Cavalini
Affiliation:
From the Divisions of Pediatric Cardiology, Heart Institute, São Paulo
Vera Demarchi Aiello
Affiliation:
Divisions of Pathology, Heart InstituteSão Paulo
*
Dr. Munir Ebaid, Instituto do Coração do Hospital das Clinicas da FMUSP, Avenida Dr. Eneas de Carvalho Aguiar 44, CEP 05403-000 São Paulo, SP, Brazil. Tel. 55-011-282-7766; Fax. 55-011-282-2354
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Summary

Absent right atrioventricular connection, with the left atrium connected to a dominant left-sided morphologically right ventricle, is a rare situation. We report four cases, demonstrating the anatomical correlations and the clinical aspects needed to make the diagnosis. We also discuss the nomenclature of this important combination.

Keywords

Absent atrioventricular connectiontricuspid atresiauniventricular heart
Type
Original Articles
Information
Cardiology in the Young , Volume 4 , Issue 4 , October 1994 , pp. 381 - 385
Copyright
Copyright © Cambridge University Press 1994

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References

1.Casta, A, Wolf, WJ, Sapire, DW. Absent right atrioventricular connexion with the left atrium connected to the morphologically right ventricle, a right-sided rudimentary left ventricle, and right juxtaposition of the atrial appendages: documentation by angiography and cross-sectional echocardiography. Int J Cardiol 1985; 7: 21–26.Google Scholar
2.Dickinson, DF, Wilkinson, JL, Anderson, KR, Smith, A, Ho, SY, Anderson, RH. The cardiac conduction system in situs ambiguus. Circulation 1979; 59: 879–885.Google Scholar
3.Anjos, R, Murdoch, I, Qureshi, S. Absence of one atrioventricular connexion—a terminologic problem. Int J Cardiol 1991; 30: 239–242.Google Scholar
4.Anderson, RH, Tynan, M. Description of complex forms of atrioventricular valvar atresia. Int J Cardiol 1991; 30: 243–247.Google Scholar
5.Ho, SY, Milo, S, Anderson, RH, Macartney, FJ, Goodwin, A, Becker, AE, Wenink, ACG, Gerlis, LM, Wilkinson, JL. Straddling atrioventricular valve with absent atrioventricular connection. Report of 10 cases. Br Heart J 1982; 47: 344–352.CrossRefGoogle ScholarPubMed
6.Shinebourne, EA, Lau, K-C, Calcaterra, G, Anderson, RH. Univentricular heart of right ventricular type: clinical, angiographic and electrocardiographic features. Am J Cardiol 1980; 46: 439–445.Google Scholar
7.Matsuda, H, Kawashima, Y, Kishimoto, H, Hirose, H, Nakano, S, Kato, H, Taniguchi, k, Nishigaki, K, Sano, T, Ogawa, M. Problems in the modified Fontan operation for univentricular heart of the right ventricular type. Circulation 1987; 76(Suppl III): III 45–III 52.Google Scholar
8.Rao, PS. Terminology: Is tricuspid atresia the correct term to use? In: Rao, PS (ed). Tricuspid Atresia. 2nd edition. Futura Publishing Inc., Mount Kisko, NY, 1992, pp 3–15.Google Scholar