Hostname: page-component-848d4c4894-5nwft Total loading time: 0 Render date: 2024-06-12T01:01:00.750Z Has data issue: false hasContentIssue false
  • English
  • Français

Atrioventricular septal defect with an imperforate right-sided component of the common atrioventricular valve: anatomic and embryologic considerations

Published online by Cambridge University Press:  10 July 2013

Lazaro E. Hernandez ,
Lazaros K. Kochilas  and
Robert H. Anderson
Lazaro E. Hernandez*
Affiliation:
Department of Pediatrics, Amplatz Children's Hospital, University of Minnesota, Minneapolis, Minnesota, United States of America
Lazaros K. Kochilas
Affiliation:
Department of Pediatrics, Amplatz Children's Hospital, University of Minnesota, Minneapolis, Minnesota, United States of America
Robert H. Anderson
Affiliation:
Department of Pediatrics, Institute of Medical Genetics, Newcastle University, Newcastle-upon-Tyne, United Kingdom
*
Correspondence to: L. E. Hernandez, MD, 2540 Riverside Ave, East 5th floor, Minneapolis, Minnesota, United States of America. Tel: 612-626-2755; Fax: 612-626-2467; E-mail: email: herna426@umn.edu
Get access Rights & Permissions [Opens in a new window]

Abstract

We describe an atypical case of an atrioventricular septal defect with a common atrioventricular junction in which the right-sided component of the common atrioventricular valve was imperforate, producing tricuspid atresia with a severely hypoplastic right ventricle and an ostium primum defect. We discuss the implications of the anatomic findings with regard to concepts of cardiac development, drawing a comparison with similar cases previously reported.

Keywords

Imperforate atrioventricular valveostium primumhypoplastic right ventricle
Type
Brief Reports
Information
Cardiology in the Young , Volume 24 , Issue 3 , June 2014 , pp. 540 - 542
Copyright
Copyright © Cambridge University Press 2013 

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

References

1. Cetta, F, Minichi, LL, Edwards, W, Dearani, J, Puga, FJ. Atrioventricular septal defects. In: Moss and Adams’ Heart Disease in Infants, Children, and Adolescents Including the Fetus and Young Adult, vol. 31, 7th edn. 2008: 646–667. Lippincott Williams & Wilkins: Philadelphia.Google Scholar
2. Valdes-Cruz, L, Cayre, RO. Atrioventricular septal defect. In: Echocardiographic Diagnosis of Congenital Heart Disease. An Embryologic and Anatomic Approach, vol. 11, 1st edn. 1999: 215–234. Lippincott-Raven: Philadelphia.Google Scholar
3. Aiello, VD, Afiune, JY, Menahem, S, Anderson, RH. Atrioventricular septal defect with coexisting tricuspid atresia. Cardiol Young 2011; 21: 299–302.Google Scholar
4. Anderson, RH, Ho, SY, Macartney, FJ, Becker, AE. The anatomy of atrioventricular septal defects. In: Quero Jimenez M, Arteaga M (eds). Pediatric Cardiology. Atrioventricular Septal Defects. Doyma, Madrid, 1988: 132–150.Google Scholar
5. Van Mierop, LHS, Alley, RD, Kausel, HW, Stranahan, A. The anatomy and embryology of the endocardial cushion defects. J thorac Cardiovasc Surg 1962; 43: 71–83.Google Scholar
6. Anderson, RH, Wessels, A, Vettukattil, JJ. Morphology and morphogenesis of atrioventricular septal defect with common atrioventricular junction. World J Pediatr Congenit Heart Surg 2010; 1: 59–67.Google Scholar
7. Van Praagh, S, Vangi, V, Sul, JH, et al. Tricuspid atresia or severe stenosis with partial common atrioventricular canal: anatomic data, clinical profile and surgical considerations. JACC 1991; 17: 932–943.Google Scholar