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Management of adults with Tetralogy of Fallot

Published online by Cambridge University Press:  09 January 2014

Richard M. Martinez ,
Jeremy M. Ringewald ,
Hector L. Fontanet ,
James A. Quintessenza  and
Jeffrey P. Jacobs
Richard M. Martinez*
Affiliation:
Johns Hopkins All Children's Heart Institute, Department of Pediatrics, University of South Florida, Pediatric Cardiology Associates/Pediatrix Medical Group, All Children's Hospital, United States of America
Jeremy M. Ringewald
Affiliation:
Johns Hopkins All Children's Heart Institute, The Congenital Heart Institute of Florida, All Children' Hospital, St. Josephs Children's Hospital of Tampa, Pediatric Cardiology Associates/Pediatrix Medical Group, United States of America
Hector L. Fontanet
Affiliation:
The Congenital Heart Institute of Florida, All Children's Hospital, Children's Hospital of Tampa, Florida Medical Clinic, University of South Florida, Saint Petersburg and Tampa, Florida, United States of America
James A. Quintessenza
Affiliation:
Johns Hopkins All Children's Heart Institute, Johns Hopkins Children's Heart Surgery, All Children's Hospital and Florida Hospital for Children, United States of America
Jeffrey P. Jacobs
Affiliation:
Johns Hopkins All Children's Heart Institute, Johns Hopkins University, Saint Petersburg, Tampa, and Orlando, Florida, United States of America
*
Correspondence to: Richard M. Martinez, MD, Johns Hopkins All Children's Heart Institute, Saint Petersburg, Florida, United States of America. Tel: (727) 434-4486; E-mail: rmarti9209@aol.com
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Abstract

Tetralogy of Fallot is the most common form of cyanotic congenital cardiac disease. Patients with previously repaired tetralogy of Fallot are the most common patients seen in the Program for Adults with Congenital Heart Disease at The Johns Hopkins All Children's Heart Institute. Guidelines for the management of these patients are available from multiple sources including The American College of Cardiology (ACC) and The American Heart Association (AHA), The Canadian Cardiovascular Society, and The European Society of Cardiology (ESC). These guidelines describe multiple components related to the care for these patients including strategies for medical follow-up, the management of arrhythmias and electrophysiological diseases, and the treatment of chronic pulmonary insufficiency and stenosis. Several new strategies are available for replacement of the pulmonary valve including transcatheter replacement of the pulmonary valve and replacement of the pulmonary valve with a self-manufactured bicuspid polytetrafluoroethylene pulmonary valve.

Keywords

Tetralogy of fallotpulmonary insufficiencypulmonary stenosisadults with congenital heart disease
Type
Original Article
Information
Cardiology in the Young , Volume 23 , Issue 6: HeartWeek 2013 , December 2013 , pp. 921 - 932
Copyright
Copyright © Cambridge University Press 2013 

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