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Pentalogy of Cantrell with double-outlet right ventricle: a case of surgical correction

Published online by Cambridge University Press:  21 December 2010

Yoshio Ootaki ,
James Strainic  and
Ross M. Ungerleider
Yoshio Ootaki*
Affiliation:
Division of Pediatric Cardiothoracic Surgery, Rainbow Babies and Children's Hospital, University Hospitals Case Medical Center, Cleveland, Ohio, United States of America
James Strainic
Affiliation:
Division of Pediatric Cardiology, Rainbow Babies and Children's Hospital, University Hospitals Case Medical Center, Cleveland, Ohio, United States of America
Ross M. Ungerleider
Affiliation:
Division of Pediatric Cardiothoracic Surgery, Rainbow Babies and Children's Hospital, University Hospitals Case Medical Center, Cleveland, Ohio, United States of America
*
Correspondence to: Dr Y. Ootaki, Division of Pediatric Cardiothoracic Surgery, Rainbow Babies and Children's Hospital, University Hospitals Case Medical Center, 11100 Euclid Avenue, Cleveland, Ohio 44106, United States of America. Tel: 216 844 3058; Fax: 216 844 3517; E-mail: y.ootaki@nifty.com
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Abstract

Pentalogy of Cantrell is characterised by a combination of severe defects in the middle of the chest including the sternum, diaphragm, heart, and abdominal wall. Mortality rate after cardiac surgery is usually high. We report a successful total correction of the cardiac defects in a case of Pentalogy of Cantrell with a double-outlet right ventricle prior to abdominal wall defect repair.

Keywords

Congenital cardiac defectcardiac surgeryomphalocele
Type
Brief Reports
Information
Cardiology in the Young , Volume 21 , Issue 2 , April 2011 , pp. 235 - 237
Copyright
Copyright © Cambridge University Press 2010

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References

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