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Successful use of long-acting octreotide for protracted gastrointestinal bleeding related to protein-losing enteropathy after the Fontan procedure: a case report

Part of: Metabolic

Published online by Cambridge University Press:  16 February 2021

Kentaro Kogawa Open the ORCID record for Kentaro Kogawa [Opens in a new window] ,
Tatsuya Ando  and
Masako Fujiwara
Kentaro Kogawa*
Affiliation:
Department of Paediatrics, The Jikei University School of Medicine, Tokyo, Japan
Tatsuya Ando
Affiliation:
Department of Paediatrics, The Jikei University School of Medicine, Tokyo, Japan
Masako Fujiwara
Affiliation:
Department of Paediatrics, The Jikei University School of Medicine, Tokyo, Japan Department of Paediatrics, Machida Municipal Hospital, Tokyo, Japan
*
Author for correspondence: Kentaro Kogawa, MD, Department of Paediatrics, Jikei University School of Medicine 3-25-8, Nishi-Shimbashi, Minato-ku, Tokyo, Japan, 105-8461. Tel: 81-(0)3-3433-1111; Fax: 81-(0)3-3435-8665. E-mail: kogawa.kentaro@scmc.pref.saitama.jp
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Abstract

Gastrointestinal bleeding complicated with protein-losing enteropathy after the Fontan procedure has been often reported in recent years, but there is no established therapy for it.

We report the case of an 18-year-old boy who suffered from abdominal pain, melena, and anaemia due to intractable haemorrhagic protein-losing enteropathy after the Fontan procedure. He was successfully treated with octreotide therapy.

Keywords

The Fontan procedureprotein-losing enteropathygastrointestinal bleedingoctreotideintramuscular injection
Type
Brief Report
Information
Cardiology in the Young , Volume 31 , Issue 8 , August 2021 , pp. 1333 - 1335
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Copyright
© The Author(s), 2021. Published by Cambridge University Press

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References

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