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Surgical ablation of a cardiac rhabdomyoma in an infant with tuberous sclerosis

Published online by Cambridge University Press:  19 August 2008

Dagmar Henglein ,
Nabil-Maurice Guirgis  and
Gérard Bloch
Dagmar Henglein*
Affiliation:
Hôpital Lariboisière, Service de Chirurgie Cardio-vasculaire, 75010 Paris, France
Nabil-Maurice Guirgis
Affiliation:
Hôpital Lariboisière, Service de Chirurgie Cardio-vasculaire, 75010 Paris, France
Gérard Bloch
Affiliation:
Hôpital Lariboisière, Service de Chirurgie Cardio-vasculaire, 75010 Paris, France
*
Dr. Dagmar Henglein, Hôpital Lariboisière, 6 rue Ambroise Paré, Service de Chirurgie Cardio-vasculaire, 75010 Paris, France. Tel: 33-1-49 95 65 91 (secretary); Tel: 33-1-49 95 84 54 (direct); Fax: 33-1-49 95 86 32
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Summary

Cardiac rhabdomyoma is a rare tumor. Because of its rate of regression, mainly in the first year of life, conservative therapy is generally suggested when diagnosis occurs in infancy. We report surgical ablation of a rhabdomyoma in a 2-month-old boy in whom the tumor extended into the subaortic outflow tract. The tumor, which had a dual attachment to the aortic and mitral valves, was safely removed without any valvar damage. We suggest immediate surgical intervention for those rhabdomyomas which are life-threatening because of their size, location, or arrhythmogenicity.

Keywords

Rhabdomyomacardiac tumor in infancy
Type
Brief Reports
Information
Cardiology in the Young , Volume 8 , Issue 2 , April 1998 , pp. 260 - 261
Copyright
Copyright © Cambridge University Press 1998

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