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Unicuspid and quadricuspid aortic valves: two case reports and literature review

Part of: Cardiac Morphology Atrial Septal Defect (ASD) Echocardiography

Published online by Cambridge University Press:  31 March 2021

Eyup Aslan Open the ORCID record for Eyup Aslan [Opens in a new window]
Eyup Aslan*
Affiliation:
Department of Pediatric Cardiology, Denizli State Hospital, Denizli, Turkey
*
Author for correspondence: Eyup Aslan, MD, Denizli State Hospital, Sirakapilar Mahallesi, Sehit Albay Karaoglanoglu Caddesi No:3 Merkezefendi, Denizli20100, Turkey.. Tel: +90 (258) 2639311, Fax: +90 (507) 5057763. E-mail: eyupaslan6@gmail.com
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Abstract

There are three cusps in a normally developed aortic valve. Abnormal excavation or fusion, during the embryological development of the aortic valve, results in a varying number of cusps. Bicuspid aortic valve is the most common, but more rarely, unicuspid and quadricuspid aortic valves can be seen.

Here, a case of a 16-year-old male with a unicommissural unicuspid aortic valve and a case of a 13-year-old female with a quadricuspid aortic valve were reported.

Keywords

Echocardiographyquadricuspid aortic valveunicuspid aortic valve
Type
Brief Report
Information
Cardiology in the Young , Volume 31 , Issue 9 , September 2021 , pp. 1538 - 1541
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Copyright
© The Author(s), 2021. Published by Cambridge University Press

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