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Benefits of magnetic resonance image scanning in progressive, bilateral, sensorineural hearing loss: a case of leptomeningeal haemosiderosis

Published online by Cambridge University Press:  04 February 2009

A Muthu ,
S Stevenson  and
P Bird
A Muthu
Affiliation:
Department of Otolaryngology – Head and Neck Surgery, Christchurch Hospital, New Zealand
S Stevenson*
Affiliation:
Department of Otolaryngology – Head and Neck Surgery, Christchurch Hospital, New Zealand
P Bird
Affiliation:
Department of Otolaryngology – Head and Neck Surgery, Christchurch Hospital, New Zealand
*
Address for correspondence: Mr S Stevenson, Department of Otolaryngology - Head and Neck Surgery, Christchurch Hospital, Private Bag 4710, Christchurch 8001, New Zealand. Fax: (+64) 3 364 0273 E-mail: scott.stevenson@cdhb.govt.nz
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Abstract

Objective:

Magnetic resonance imaging is a routine investigation in cases of asymmetric sensorineural hearing loss, but it is not routinely used to investigate bilateral sensorineural hearing loss.

Method:

This case report illustrates the benefits of magnetic resonance image scanning in the latter patient group.

Results:

A 53-year-old man with rapidly progressive, symmetrical, bilateral, sensorineural hearing loss was found also to have anosmia, imbalance and incoordination. Magnetic resonance image scanning demonstrated leptomeningeal haemosiderosis. Progressive, bilateral, sensorineural hearing loss is the most common presentation of this condition and magnetic resonance imaging is the diagnostic investigation of choice.

Conclusion:

There are potential treatments for leptomeningeal haemosiderosis which prevent further irreversible damage, if a bleeding source can be found. Hearing loss may be due to cochlear or retrocochlear pathology. Cochlear implantation may be indicated.

Keywords

Leptomeningeal HemosiderosisSuperficial SiderosisSensorineural Hearing LossMagnetic Resonance Imaging
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 123 , Issue 11 , November 2009 , pp. 1266 - 1270
Copyright
Copyright © JLO (1984) Limited 2009

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