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Article

Functional near-tricuspid atresia in a patient with absent pulmonary valve and an intact ventricular septum

  • Yasunobu Miki (a1), Toshikatsu Tanaka (a1) and Yoshihiro Oshima (a2)
Abstract

Absent pulmonary valve with an intact ventricular septum is a rare malformation. We report a case of absent pulmonary valve and intact ventricular septum with functional near-tricuspid atresia caused by pulmonary regurgitation. Initial palliation with main pulmonary artery ligation and bilateral pulmonary artery banding was performed at 1 day of age. More antegrade flow across the tricuspid valve was recognised postoperatively, resulting in a successful right ventricular outflow tract reconstruction by a hand-sewn bileaflet polytetrafluoroethylene valve and modified Blalock–Taussig shunt at 11 days of age.

Copyright
© Cambridge University Press 2016 
Corresponding author
Correspondence to: Y. Miki, Department of Cardiology, Kobe Children’s Hospital, 1-6-7 Minatojimamimamimachi, Chuo-ku, Kobe, Hyogo 650-0047, Japan. Tel: +81 078 945 7300; Fax: +81 078 302 1023; E-mail: mkysnb@gmail.com
References
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Cardiology in the Young
  • ISSN: 1047-9511
  • EISSN: 1467-1107
  • URL: /core/journals/cardiology-in-the-young
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