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Functional tricuspid stenosis: a rare presentation of suspected rhabdomyoma as congenital cyanotic heart disease

Published online by Cambridge University Press:  12 January 2017

Anishkumar Nair Open the ORCID record for Anishkumar Nair [Opens in a new window] ,
Gopalan Nair Rajesh  and
Chakanalil Govindan Sajeev
Anishkumar Nair*
Affiliation:
Department of Cardiology, Government Medical College, Kozhikode, Kerala, India
Gopalan Nair Rajesh
Affiliation:
Department of Cardiology, Government Medical College, Kozhikode, Kerala, India
Chakanalil Govindan Sajeev
Affiliation:
Department of Cardiology, Government Medical College, Kozhikode, Kerala, India
*
Correspondence to: Dr N. Anishkumar, MD, Senior Resident, Department of Cardiology, Government Medical College, Kozhikode, Kerala 673008, India. Tel: +918281054567; Fax: +91-495-2355331; E-mail: dr.anish84@gmail.com
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Abstract

Cardiac tumours in newborns are often asymptomatic and can be sporadically detected on routine screening unless they result in intractable arrhythmias or haemodynamically significant obstructions causing heart failure. Their presentation as a cause of congenital cyanosis is never anticipated. We report a rare case of a newborn presenting with congenital cyanosis consequent to suspected cardiac rhabdomyoma causing tricuspid inflow obstruction. Our experience with this patient with two large cardiac masses illustrates the significance of its inclusion in the differential diagnosis of perinatal cyanosis, as early detection and surgical management might be the only lifesaving options, if performed well in time.

Keywords

Cardiac rhabdomyomacyanosistricuspid inflow obstructiontuberous sclerosis
Type
Brief Report
Information
Cardiology in the Young , Volume 27 , Issue 4 , May 2017 , pp. 808 - 811
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Copyright
© Cambridge University Press 2017 

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References

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