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Recent advances in superior semicircular canal dehiscence syndrome

Published online by Cambridge University Press:  06 February 2015

G Chilvers  and
I McKay-Davies
G Chilvers*
Affiliation:
ENT Department, St Michael's Hospital, University Hospitals Bristol, UK
I McKay-Davies
Affiliation:
ENT Department, St Michael's Hospital, University Hospitals Bristol, UK
*
Address for correspondence: Mr G ChilversENT Department, St Michaels Hospital, University Hospitals Bristol, Southwell Street, Bristol, BS2 8EG, UK, E-mail: geoffreyschilvers@gmail.com
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Abstract

Objective:

This study aimed to review the current advances in superior semicircular canal dehiscence syndrome and to ascertain its aetiology, whether dehiscence size correlates with symptoms, signs and investigation results, the best investigations, and its surgical management.

Methods:

A literature search using the key words ‘superior semicircular canal dehiscence’ was performed using the Allied and Complementary Medicine Database and the Embase, Health Management Information Consortium, Medline, PsycINFO, British Nursing Index, Cinahl and Health Business Elite databases for the period January 2009 to May 2014. Systematic reviews, meta-analyses, randomised controlled trials, prospective and retrospective case series, case reports, and observational studies were included.

Results:

Of the 205 papers identified, 35 were considered relevant.

Conclusion:

The aetiology of superior semicircular canal dehiscence syndrome is unclear. Dehiscence size significantly affects the air–bone gap and ocular vestibular evoked myogenic potential thresholds. Computed tomography evaluation has a high false positive rate. The middle cranial fossa approach is the surgical standard for treating this syndrome; however, the transmastoid approach is gaining popularity.

Keywords

Inner EarVestibular Evoked Myogenic PotentialsSemicircular CanalsVertigo
Type
Review Articles
Information
The Journal of Laryngology & Otology , Volume 129 , Issue 3 , March 2015 , pp. 217 - 225
Copyright
Copyright © JLO (1984) Limited 2015 

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