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Elective left pulmonary artery embolisation for pulmonary arteriovenous malformations secondary to cavopulmonary anastomoses not responsive to heart transplantation: a case report

Part of: Interventional Cardiology Functionally Univentricular Heart

Published online by Cambridge University Press:  13 September 2019

Caroline M. Bebawy Open the ORCID record for Caroline M. Bebawy [Opens in a new window] ,
Brent M. Gordon  and
Matthew J. Bock Open the ORCID record for Matthew J. Bock [Opens in a new window]
Caroline M. Bebawy
Affiliation:
Loma Linda University School of Medicine, Loma Linda, CA, USA
Brent M. Gordon
Affiliation:
Division of Pediatric Cardiology, Loma Linda University Children’s Hospital, Loma Linda, CA, USA
Matthew J. Bock*
Affiliation:
Division of Pediatric Cardiology, Loma Linda University Children’s Hospital, Loma Linda, CA, USA
*
Author for correspondence: Matthew J. Bock, Loma Linda University Medical Center,, 11234 Anderson St., MC-4434, Loma Linda, CA 92354, USA. Tel: 909-558-8083; Fax: 888-365-2421; E-mail: mbock@llu.edu
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Abstract

A 10-year-old female with heterotaxy-asplenia and complex CHD developed pulmonary arteriovenous malformations with associated cyanosis after Fontan completion. She underwent orthotopic heart transplantation, but her pulmonary arteriovenous malformations persisted with progressive worsening cyanosis. Elective transcatheter left pulmonary artery embolisation was performed 2 years post-transplant, which successfully normalised her oxygen saturation without a significant increase in pulmonary artery pressure.

Keywords

Pulmonary arteriovenous malformationspulmonary artery embolisationheterotaxy syndromecomplex CHDheart transplantationpediatrics
Type
Brief Report
Information
Cardiology in the Young , Volume 29 , Issue 11 , November 2019 , pp. 1404 - 1406
Copyright
© Cambridge University Press 2019 

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