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Arrhythmogenic right ventricular dysplasia/cardiomyopathy

Published online by Cambridge University Press:  13 January 2017

Gabriela M. Orgeron  and
Jane E. Crosson
Gabriela M. Orgeron
Affiliation:
Division of Cardiology, Bloomberg Children’s Center, Johns Hopkins University, Baltimore, Maryland, United States of America
Jane E. Crosson*
Affiliation:
Division of Pediatric Cardiology, Bloomberg Children’s Center, Johns Hopkins University, Baltimore, Maryland, United States of America
*
Correspondence to: Dr J. E. Crosson, Johns Hopkins Children’s Center, 1800 Orleans Street, Room 2319, Baltimore, MD 21287, United States of America. Tel: 410 955 5987; Fax: 410-614-9942; E-mail: jcrosso@jhmi.edu
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Abstract

Arrhythmogenic right ventricular dysplasia/cardiomyopathy is an inherited cardiomyopathy characterised by ventricular arrhythmias and an increased risk of sudden cardiac death. Arrhythmogenic right ventricular dysplasia/cardiomyopathy diagnosis is based on criteria that take into account electrical and structural cardiac abnormalities, as well as mutation analysis. Appropriate pharmacological therapy and the prevention of sudden death with implantable defibrillators are important in the management of these patients. Exercise is considered an important environmental factor for the development and progression of the disease.

Keywords

Arrhythmogenic right ventricular dysplasia/cardiomyopathyexercisechildrenyoung athletes
Type
Original Articles
Information
Cardiology in the Young , Volume 27 , Supplement S1: Sudden Cardiac Arrest in the Young: A Contemporary Perspective , January 2017 , pp. S57 - S61
Copyright
© Cambridge University Press 2017 

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