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Rare case of septum primum malposition defect in dextrocardia and situs inversus totalis without heterotaxy syndrome

Part of: Cardiac Morphology

Published online by Cambridge University Press:  26 December 2018

Simone Jhaveri ,
Francine Erenberg  and
Malek Yaman
Simone Jhaveri*
Affiliation:
Department of Pediatric Cardiology, Cleveland Clinic Children’s, Cleveland, OH, USA
Francine Erenberg
Affiliation:
Department of Pediatric Cardiology, Cleveland Clinic Children’s, Cleveland, OH, USA
Malek Yaman
Affiliation:
Department of Pediatric Cardiology, Cleveland Clinic Children’s, Cleveland, OH, USA
*
Author for correspondence: Simone Jhaveri, 9500 Euclid Avenue, Cleveland, OH 44195, USA. Tel: +1 216-337-4433; Fax: +1 216-445-5679; E-mail: jhavers@ccf.org
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Abstract

Septum primum malposition defect is an extremely rare CHD and is often found in patients with visceral heterotaxy, particularly of the polysplenia type. We describe a unique patient with dextrocardia, situs inversus totalis, and bilateral superior vena caval veins without heterotaxy syndrome who was diagnosed with an interatrial defect and partial anomalous pulmonary venous drainage due to malposition of the septum primum.

Keywords

Septum primum malpositionpartial anomalous pulmonary venous drainageheterotaxysitus inversus totalisdextrocardia
Type
Brief Report
Information
Cardiology in the Young , Volume 29 , Issue 3 , March 2019 , pp. 419 - 421
Copyright
© Cambridge University Press 2018 

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Footnotes

Cite this article: Jhaveri S, Erenberg F, Yaman M. (2019) Rare case of septum primum malposition defect in dextrocardia and situs inversus totalis without heterotaxy syndrome. Cardiology in the Young29: 419–421. doi: 10.1017/S1047951118002263

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