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Case 83 - Aggressive fibromatosis (desmoid tumor)

from Section 12 - Tumors/Miscellaneous

Published online by Cambridge University Press:  05 July 2013

D. Lee Bennett
Affiliation:
University of Iowa
Georges Y. El-Khoury
Affiliation:
University of Iowa
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Summary

Imaging description

The principal role of imaging is in the management of aggressive fibromatosis, as well as staging in pre-operative planning and for the follow-up of progression in patients who are treated non-operatively. In post-operative follow-up imaging plays a key role in detecting recurrence. On conventional radiographs, aggressive fibromatosis is either undetectable or identified as an amorphous soft tissue mass. Calcification within the mass is uncommon. On rare occasions radiography may show bony infiltration or destruction of adjacent bones (Figure 83.1). As with most soft tissue tumors, MR is the best imaging modality for assessing aggressive fibromatosis. The majority of lesions appear iso- to mildly hyperintense relative to muscle on T1-weighted image. The T1 signal intensity is usually homogeneous. On T2-weighted images the majority of lesions are hyperintense relative to muscle (Figure 83.1). In about one third of the patients aggressive fibromatosis displays lower signal intensity than muscle on T2-weighted images (Figure 83.2). These lesions have less cellularity and more collagen than tumors with high signal-intensity T2-weighted images. The hyperintense lesions on T2-weighted images are typically heterogeneously hyperintense. Bands of low signal intensity within the lesion on all sequences are reported to occur in about two thirds of cases. This is in concordance with previously published data. After injection of IV gadolinium, these tumors show either avid or moderate enhancement.

Type
Chapter
Information
Pearls and Pitfalls in Musculoskeletal Imaging
Variants and Other Difficult Diagnoses
, pp. 195 - 198
Publisher: Cambridge University Press
Print publication year: 2013

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References

Casillas, J, Sais, GJ, Greve, JL et al. Imaging of intra-and extraabdominal desmoid tumors. RadioGraphics 1991;11:959–968.CrossRefGoogle ScholarPubMed
Griffiths, HJ, Robinson, K, Bonfiglio, TA.Aggressive fibromatosis. Skeletal Radiol 1983;9:179–184.CrossRefGoogle ScholarPubMed
Lee, JC, Thomas, JM, Phillips, S et al. Aggressive fibromatosis: MRI features with pathologic correlation. AJR Am J Roentgenol 2006;186:247–254.CrossRefGoogle ScholarPubMed
Nakayama, T, Tsuboyama, T, Toguchida, J et al. Natural course of desmoid-type fibromatosis. J Orthop Sci 2008;13:51–55.CrossRefGoogle ScholarPubMed
O’Keefe, F, Kim, EE, Wallace, S.Magnetic resonance imaging in aggressive fibromatosis. Clin Radiol 1990;42:170–173.CrossRefGoogle ScholarPubMed
Rock, MG, Pritchard, DJ, Reiman, HM et al. Extra-abdominal desmoid tumors. J Bone Joint Surg 1984;66-A;1369–1374.CrossRefGoogle Scholar
Sundaram, M, Duffrin, H, McGuire, MH, Vas, W.Synchronous multicentric desmoid tumors (aggressive fibromatosis) of the extremities. Skeletal Radiol 1988;17:16–19.CrossRefGoogle ScholarPubMed
Sundaram, M, McGuire, MH, Schajowicz, F.Soft-tissue masses: histologic basis for decreased signal (short T2) on T2-weighted MR images. AJR Am J Roentgenol 1987;148:1247–1250.CrossRefGoogle ScholarPubMed

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