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Vein of Galen Malformation with Cerebral Calcification: A Reversible Cause of Neurodegenerative Disease

Published online by Cambridge University Press:  18 September 2015

Stephen J. Phillips ,
Joseph M. Dooley  and
Peter R. Camfield
Stephen J. Phillips
Affiliation:
Departments of Medicine and Pediatrics, Dalhousie University, Halifax, Nova Scotia
Joseph M. Dooley*
Affiliation:
Departments of Medicine and Pediatrics, Dalhousie University, Halifax, Nova Scotia
Peter R. Camfield
Affiliation:
Departments of Medicine and Pediatrics, Dalhousie University, Halifax, Nova Scotia
*
Izaak Walton Killam Hospital for Children, P.O. Box 3070, Halifax, Nova Scotia, Canada B3J 3G9
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Abstract:

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This paper reports two children who had mental retardation as the predominant manifestation of vein of Galen malformations. C.T. scans demonstrated extensive intracerebral calcification. Surgery reversed the progressive downhill course in one patient and may have arrested further deterioration in the other. The pathophysiological mechanisms underlying the clinical and radiographic features are discussed.

Type
Original Articles
Information
Canadian Journal of Neurological Sciences , Volume 13 , Issue 2 , May 1986 , pp. 103 - 106
Copyright
Copyright © Canadian Neurological Sciences Federation 1986

References

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