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Gastrointestinal haemorrhage due to lymphangiectasia caused by protein-losing enteropathy in the Fontan circulation

Published online by Cambridge University Press:  27 June 2017

Pauline Gras ,
Frédéric Gottrand  and
François Godart
Pauline Gras*
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, Faculty of Medicine, Regional University Hospital Center of Lille, Lille, France
Frédéric Gottrand
Affiliation:
Division of Hepatology, Gastroenterology and Nutrition, Faculty of Medicine, Jeanne de Flandre Children’s Hospital, Regional University Hospital Center of Lille, Lille, France
François Godart
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, Faculty of Medicine, Regional University Hospital Center of Lille, Lille, France
*
Correspondence to: P. Gras, Cardiologie Pédiatrique et Congénitale, Hôpital Cardiologique, Centre Hospitalier Universitaire De Lille, Université Lille 2, Boulevard du Professeur Jules Leclercq, 59037 Lille, France, Tel: +33 320445062; Fax: +33 3320445456; E-mail: pauline.gras21@gmail.com
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Abstract

We report the case of a 14-year-old boy with severe protein-losing enteropathy after Fontan surgery that led to lymphangiectasia, which caused gastrointestinal haemorrhage and required invasive treatment to stop the bleeding. Through this case and a review of the literature on protein-losing enteropathy after Fontan surgery, we highlight a rare and serious presentation of the disease and the difficulties of diagnosis and management.

Keywords

Tricuspid atresiaprotein-losing enteropathylymphangiectasis, intestinalgastrointestinal haemorrhage
Type
Brief Report
Information
Cardiology in the Young , Volume 27 , Issue 8 , October 2017 , pp. 1641 - 1643
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Copyright
© Cambridge University Press 2017 

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