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Left aortic arch with right descending aorta and severe coarctation: an unusual “vascular clamp” with airway compression

Part of: Ventricular Septal Defect (VSD) Cardiac Morphology

Published online by Cambridge University Press:  13 June 2018

Ronak Sheth ,
Roy Varghese  and
Kothandam Sivakumar
Ronak Sheth
Affiliation:
Department of Pediatric Cardiology, Madras Medical Mission, Chennai, India
Roy Varghese
Affiliation:
Department of Pediatric Cardiology, Madras Medical Mission, Chennai, India
Kothandam Sivakumar*
Affiliation:
Department of Pediatric Cardiology, Madras Medical Mission, Chennai, India
*
Author for correspondence: Dr K. Sivakumar, MD, DM, Head of Department of Pediatric Cardiology, Institute of Cardiovascular Diseases, Madras Medical Mission, 4A, Dr J J Nagar, Mogappair, Chennai 600089, India. Tel: +91 9444449966; Fax: +91 44 26565859; E-mail: drkumarsiva@hotmail.com
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Abstract

Left aortic arch with right descending aorta is a rare congenital anomaly. We describe the clinical presentation of this unusual anomaly associated with cardiorespiratory compromise from severe aortic obstruction and left main bronchus compression. The anatomical peculiarities, embryological basis, and surgical solutions are presented.

Keywords

Aortic archcircumflex aortaembryology of aortic archaortic translocationcoarctation
Type
Brief Report
Information
Cardiology in the Young , Volume 28 , Issue 8 , August 2018 , pp. 1056 - 1058
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Copyright
© Cambridge University Press 2018 

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Footnotes

Cite this article: Sheth R, Varghese R, Sivakumar K. (2018) Left aortic arch with right descending aorta and severe coarctation: an unusual “vascular clamp” with airway compression. Cardiology in the Young28: 1056–1058. doi: 10.1017/S1047951118000665

References

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