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Chapter 13 - Miscellaneous Skeletal and Connective Tissue Disorders

Published online by Cambridge University Press:  26 January 2024

By
Caroline S. Grange  and
Sally Anne Shiels
Edited by
David R. Gambling ,
M. Joanne Douglas  and
Grace Lim
David R. Gambling
Affiliation:
University of California, San Diego
M. Joanne Douglas
Affiliation:
University of British Columbia, Vancouver
Grace Lim
Affiliation:
University of Pittsburgh
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Summary

This chapter discusses a variety of miscellaneous conditions found during pregnancy, each with different degrees of rarity. It focuses on the pathophysiologic changes that occur with each disease in order to highlight the impact on both anesthetic and obstetric management. However, as some of the conditions described have a wide and varied organ involvement, firm management conclusions cannot be made. Each case should be assessed individually and may necessitate a multidisciplinary approach involving obstetricians, anesthesiologists, and neonatologists.

Keywords

Gorlin syndromeNoonan syndromeneurofibromatosisVon Hippel-Lindau diseaseEhlers-Danlos syndrometuberous sclerosisMyasthenia gravisFriedreich ataxiaMarfan syndromeArthrogryposis Multiplex CongenitaOsteogenesis imperfecta
Type
Chapter
Information
Obstetric Anesthesia and Uncommon Disorders , pp. 175 - 205
Publisher: Cambridge University Press
Print publication year: 2024

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