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Anatomy and echocardiography of discordant atrioventricular connections

Published online by Cambridge University Press:  13 October 2006

William T. Mahle ,
Gerald R. Marx  and
Robert H. Anderson
William T. Mahle
Affiliation:
Children's Healthcare of Atlanta and the Emory University School of Medicine, Atlanta, Georgia, United States of America
Gerald R. Marx
Affiliation:
Children's Hospital, Harvard University School of Medicine, Boston, Massachusetts, United States of America
Robert H. Anderson
Affiliation:
Cardiac Unit, University College London Institute of Child Health, London, United Kingdom
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Abstract

The most appropriate way of describing the congenital cardiac malformations unified because the atrial chambers are joined across the atrioventricular junctions to morphologically inappropriate ventricles has long been contentious. In the past, the lesions have been described in such arcane terms as mixed levocardia,1 while “ventricular inversion” still retains it currency in some circles. As we will show in this review, the abnormal arrangements at the atrioventricular junctions can be found with various patterns, but most frequently the patients also have the arterial trunks arising from morphologically inappropriate ventricles. This combination is best described as congenitally corrected transposition, and will form the focus of our review. It is salutary to note that, when von Rokitansky gave the first description of this combination,2 one of his illustrations was ideally suited to aid the understanding of modern-day echocardiographers (Fig. 1). We hope to emulate von Rokitansky in our own review.

Keywords

Congenitally corrected transpositionl-transpositionventricular inversion
Type
Discordant Atrioventricular Connections
Information
Cardiology in the Young , Volume 16 , Supplement S3: Controversies and Challenges of the Atrioventricular Junctions and Other Challenges Facing Paediatric Cardiovascular Practitioners and their Patients , September 2006 , pp. 65 - 71
Copyright
© 2006 Cambridge University Press

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