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Aortic valvar atresia with a normal-sized left ventricle in an adolescent

Published online by Cambridge University Press:  03 January 2024

Sourabh Goswami ,
Rengarajan Rajagopal Open the ORCID record for Rengarajan Rajagopal [Opens in a new window]  and
Surender Deora
Sourabh Goswami
Affiliation:
All India Institute of Medical Sciences, Jodhpur, RJ, India
Rengarajan Rajagopal*
Affiliation:
All India Institute of Medical Sciences, Jodhpur, RJ, India
Surender Deora
Affiliation:
All India Institute of Medical Sciences, Jodhpur, RJ, India
*
Corresponding author: Rengarajan Rajagopal; Email: rajagopalr@aiimsjodhpur.edu.in
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Abstract

Atresia of the aortic valve is usually associated with hypoplasia of the mitral valve and the left ventricle. In very rare cases, a ventricular septal defect may be associated with aortic atresia, when left ventricle and mitral valve are normal-sized, due to the presence of an outflow for the left ventricle through the ventricular septal defect. We present the multi-modality imaging findings of an adolescent girl who presented with breathlessness and was later found to have aortic valvar atresia with a normal-sized left ventricle.

Keywords

aortic valveaortic atresiacongenital heart disease
Type
Brief Report
Information
Cardiology in the Young , Volume 34 , Issue 2 , February 2024 , pp. 462 - 464
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Copyright
© The Author(s), 2024. Published by Cambridge University Press

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