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Idiopathic dilatation of the right atrium: a not so benign entity

Published online by Cambridge University Press:  05 June 2020

Carin Walter Open the ORCID record for Carin Walter [Opens in a new window] ,
Joaquim Bartrons ,
Olga Gómez ,
José M. Caffarena  and
Juan M. Carretero
Carin Walter
Affiliation:
Paediatric Cardiology, Hospital Sant Joan de Déu, Barcelona, Spain
Joaquim Bartrons
Affiliation:
Paediatric Cardiology, Hospital Sant Joan de Déu, Barcelona, Spain
Olga Gómez
Affiliation:
Foetal i+D Foetal Medicine Research Center, BCNatal – Barcelona Centre for Maternal-Foetal and Neonatal Medicine (Hospital Clínic and Hospital Sant Joan de Déu), Institut Clínic de Ginecologia Obstetricia i Neonatologia, Institut d’Investigacions Biomèdiques August Pi i Sunyer, Universitat de Barcelona, Centre for Biomedical Research on Rare Diseases (CIBER-ER), Barcelona, Spain
José M. Caffarena
Affiliation:
Paediatric Cardiology, Hospital Sant Joan de Déu, Barcelona, Spain
Juan M. Carretero*
Affiliation:
Paediatric Cardiology, Hospital Sant Joan de Déu, Barcelona, Spain
*
Author for correspondence: J. Manuel Carretero Bellón, MD, Paediatric Cardiology Department, Hospital San Juan de Dios, Pg. Sant Joan de Déu 2, 08950Esplugues de Llobregat, Spain. Tel: +34 93 253 21 00; Fax: +34 93 203 39 59. E-mail: jcarretero@sjdhospitalbarcelona.org
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Abstract

Idiopathic dilatation of the right atrium is an isolated enlargement of the right atrium in the absence of other cardiac lesions. This rare anomaly has a clinical spectrum ranging from asymptomatic to heart failure or even sudden death. It can be associated with atrial arrhythmias and thrombus formation. Antiplatelet therapy is prescribed in most cases reported in the literature, and reduction plasty is indicated when there is rapid growth of the right atrium, compression of adjacent structures, or refractory arrhythmias. We report four cases of idiopathic dilatation of the right atrium diagnosed during prenatal screening. We describe the intrauterine course and management in postnatal life until early childhood.

Keywords

Idiopathic dilatationright atriumCHDatrial enlargementatrial surgery
Type
Review Article
Information
Cardiology in the Young , Volume 30 , Issue 7 , July 2020 , pp. 919 - 922
Copyright
© The Author(s), 2020. Published by Cambridge University Press

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