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Successful coil embolisation of tortuous portosystemic venous shunts using a steerable microcatheter in a patient with polysplenia after a Fontan-type operation

Published online by Cambridge University Press:  12 April 2023

Yoko Kawai Open the ORCID record for Yoko Kawai [Opens in a new window] ,
Yusuke Kita  and
Kosuke Nishikawa
Yoko Kawai*
Affiliation:
Department of Pediatrics, Kyoto Prefectural University of Medicine, Kyoto, Japan
Yusuke Kita
Affiliation:
Department of Pediatrics, Kyoto Prefectural University of Medicine, Kyoto, Japan
Kosuke Nishikawa
Affiliation:
Department of Pediatrics, Kyoto Prefectural University of Medicine, Kyoto, Japan
*
Address for correspondence: Dr Y. Kawai, MD, Department of Pediatrics, Kyoto Prefectural University of Medicine, Kawaramachi-Hirokoji, Kamigyo-ku, Kyoto, Japan. Tel.: +81 75 251 5111. E-mail: y-kiwi@koto.kpu-m.ac.jp
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Abstract

Portosystemic venous shunts occur in patients with polysplenia after the Fontan operation. In the long term, these shunts are associated with hyperammonaemia and portal-systemic encephalopathy. Since some shunts are long and tortuous, catheter interventions to close them could be challenging. Instead, a steerable microcatheter could be used for coil embolisation of tortuous portosystemic venous shunts.

Keywords

Portosystemic venous shuntpolysplenia syndromefontan operationcoil embolisation
Type
Brief Report
Information
Cardiology in the Young , Volume 33 , Issue 9 , September 2023 , pp. 1781 - 1783
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Copyright
© The Author(s), 2023. Published by Cambridge University Press

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