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Sudden death in an adult with a small ventricular septal defect and an aneurysmal membranous septum

Published online by Cambridge University Press:  19 August 2008

B Sarubbi ,
L M Gerlis ,
S Y Ho  and
J Somerville
B Sarubbi
Affiliation:
Department of Paediatrics, National Heart and Lung Institute, Imperial College School of Medicine, London
L M Gerlis*
Affiliation:
Department of Paediatrics, National Heart and Lung Institute, Imperial College School of Medicine, London
S Y Ho
Affiliation:
Department of Paediatrics, National Heart and Lung Institute, Imperial College School of Medicine, London
J Somerville
Affiliation:
Jane Somerville Grown-up Congenital Heart Unit, The Royal Brompton Hospital, London
*
Dr L M Gerlis, Imperial College School of Medicine, National Heart and Lung Institute, Dovehouse Street, London SW3 6LYUK
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Abstract

An apparently healthy man of 26 years of age suddenly died. He was known to have had a small ventricular septal defect and complete right bundle branch block from early childhood. At post-mortem examination the small ventricular septal defect was found associated with an aneurysm of the membranous septum. Histological examination showed a normal atrioventricular node and bundle, adjacent to the aneurysm. There was fibrous interruption at the commencement of the right bundle branch, which was considered the basis of the bundle branch block. It was also considered that the right bundle branch block was of the hereditary type and that this, rather than the aneurysm of the membranous septum, was responsible for the unexpected death.

Keywords

Right bundle branch block-hereditaryaneurysm of membranous septumsudden death
Type
Clinico-Pathological Correlation
Information
Cardiology in the Young , Volume 9 , Issue 1 , January 1999 , pp. 99 - 103
Copyright
Copyright © Cambridge University Press 1999

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