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Tricuspid atresia with absent pulmonary valve and intact ventricular septum: successful bidirectional cavopulmonary anastomosis with complete exclusion of the right ventricle

Part of: Functionally Univentricular Heart Surgery

Published online by Cambridge University Press:  26 November 2019

Cheul Lee Open the ORCID record for Cheul Lee [Opens in a new window] ,
Kyung Min Kim ,
Jae Young Lee  and
Jihong Yoon
Cheul Lee*
Affiliation:
Department of Thoracic and Cardiovascular Surgery, Seoul St. Mary’s Hospital, College of Medicine, The Catholic University of Korea, Seoul, Republic of Korea
Kyung Min Kim
Affiliation:
Department of Pediatrics, Seoul St. Mary’s Hospital, College of Medicine, The Catholic University of Korea, Seoul, Republic of Korea
Jae Young Lee
Affiliation:
Department of Pediatrics, Seoul St. Mary’s Hospital, College of Medicine, The Catholic University of Korea, Seoul, Republic of Korea
Jihong Yoon
Affiliation:
Department of Pediatrics, Seoul St. Mary’s Hospital, College of Medicine, The Catholic University of Korea, Seoul, Republic of Korea
*
Author for correspondence: C. Lee, MD, Department of Thoracic and Cardiovascular Surgery, Seoul St. Mary’s Hospital, College of Medicine, The Catholic University of Korea, 222 Banpo-daero, Seocho-gu, Seoul 06591, Republic of Korea. Tel: +82 2 2258 6131; Fax: +82 2 594 8644; E-mail: tscheul@hanmail.net
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Abstract

Tricuspid atresia with absent pulmonary valve and intact ventricular septum is an extremely rare cardiac malformation, historically associated with a poor prognosis. Only a few cases with successful surgical palliation have been reported in the literature. We present the case of an 8-month-old infant with this malformation who underwent successful bidirectional cavopulmonary anastomosis with complete exclusion of the right ventricle.

Keywords

Tricuspid atresiaabsent pulmonary valveintact ventricular septumbidirectional cavopulmonary anastomosis
Type
Brief Report
Information
Cardiology in the Young , Volume 30 , Issue 1 , January 2020 , pp. 126 - 128
Copyright
© Cambridge University Press 2019

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References

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