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Pulmonary atresia with intact ventricular septum, right-sided aortic arch, and an aorto-pulmonary collateral artery

Published online by Cambridge University Press:  19 August 2008

Chandrakant R. Patel ,
Michael L. Spector  and
Kenneth G. Zahka
Chandrakant R. Patel*
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, and Department of Cardiothoracic Surgery, Rainbow Babies and Children's Hospital, Case Western Reserve University School of Medicine, Cleveland, OH, USA
Michael L. Spector
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, and Department of Cardiothoracic Surgery, Rainbow Babies and Children's Hospital, Case Western Reserve University School of Medicine, Cleveland, OH, USA
Kenneth G. Zahka
Affiliation:
Department of Pediatrics, Division of Pediatric Cardiology, and Department of Cardiothoracic Surgery, Rainbow Babies and Children's Hospital, Case Western Reserve University School of Medicine, Cleveland, OH, USA
*
Chandrakant R Patel, MBBS, Rainbow Babies and Childrens Hospital, Case Western Reserve University, 11100 Euclid Avenue, Cleveland, OH 44106, USA. Tel: +1 (216) 8443275; fax: +1 (216) 844478.
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Abstract

Described is a rare association in a patient with the heart in the left chest, namely pulmonary atresia with intact ventricular septum, fistulous coronary arterial connections, a right-sided aortic arch and an aorto-pulmonary collateral artery feeding one lung. The pulmonary arteries were non-confluent, with the right lung supplied by the right arterial duct originating from the under surface of the right-sided aortic arch, and the left lung supplied through the aorto-pulmonary collateral artery arising from the descending aorta. The surgical management is different in the setting of non-confluent pulmonary arteries.

Keywords

Pulmonary atresia with intact ventricular septumaorto-pulmonary collateral arteryright-sided aortic arch
Type
Brief Reports
Information
Cardiology in the Young , Volume 9 , Issue 5 , September 1999 , pp. 512 - 515
Copyright
Copyright © Cambridge University Press 1999

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References

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