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Sudden death due to aortic pathology

Published online by Cambridge University Press:  13 January 2017

John Papagiannis
John Papagiannis*
Affiliation:
Division of Cardiology, Children’s Mercy Hospital, Kansas City, Missouri, United States of America
*
Correspondence to: J. Papagiannis, Director of Electrophysiology, Division of Cardiology, Children’s Mercy Hospital, Kansas City, MO 64112, United States of America. Tel: 816 234 3000; E-mail: jpapagiannis@cmh.edu
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Abstract

Sudden death from aortic dissection of an ascending aortic aneurysm is an uncommon but important finding in all series of sudden death in young, apparently healthy athletes. Individuals at risk include those having any of a variety of conditions in which structural weakness of the ascending aorta predisposes to pathological dilation under prolonged periods of increased wall stress. These conditions include Marfan syndrome, Loeys–Dietz syndrome, bicuspid aortic valve, and the vascular form of Ehlers–Danlos syndrome. Diagnostic criteria, surveillance strategies, medical management, and surgical indications are discussed. Finally, the current recommendations for sports participation are provided.

Keywords

Aortic dissectionaortic aneurysmMarfan syndromeLoeys–Dietz syndromebicuspid aortic valve
Type
Original Articles
Information
Cardiology in the Young , Volume 27 , Supplement S1: Sudden Cardiac Arrest in the Young: A Contemporary Perspective , January 2017 , pp. S36 - S42
Copyright
© Cambridge University Press 2017 

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