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Paroxysmal complete atrioventricular block in a patient with pulmonary atresia and intact ventricular septum

  • Akash R. Patel (a1), David Goldberg (a1) and Maully Shah (a1)
  • DOI:
  • Published online: 13 October 2010

Sudden death in pulmonary atresia and intact ventricular septum with right ventricular dependent coronary circulation is a well-established complication, and is thought to be caused by myocardial ischaemia. We report a case of paroxysmal complete atrioventricular block that raises the possibility of an additional mechanism of sudden death.

Corresponding author
Correspondence to: Dr A. R. Patel, MD, Division of Cardiology, Department of Pediatrics, The Children’s Hospital of Philadelphia, University of Pennsylvania School of Medicine, 34th Street and Civic Center Blvd, Philadelphia, Pennsylvania 19104, United States of America. Tel: 215 590 2230; Fax: 215 590 5825; E-mail:
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Cardiology in the Young
  • ISSN: 1047-9511
  • EISSN: 1467-1107
  • URL: /core/journals/cardiology-in-the-young
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