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    This article has been cited by the following publications. This list is generated based on data provided by CrossRef.

    Kuo, Chin-Lung Chen, Paul Chih-Hsueh Li, Wing-Yin and Chu, Pen-Yuan 2015. Retiform Hemangioendothelioma of the Neck. Journal of Pathology and Translational Medicine, Vol. 49, Issue. 2, p. 171.

    Liu, Qingqing Ouyang, Ruoyun Chen, Ping and Zhou, Rui 2015. A case report of retiform hemangioendothelioma as pleural nodules with literature review. Diagnostic Pathology, Vol. 10, Issue. 1,

    Jothi, Ezhil Arasan Sundaram, Muthuchitra Namasivayam, Jeyalakshmidevi and Jothi, Mathivanan 2014. A Rare Presentation of Retiform Hemangioendothelioma in the External Auditory Canal. Case Reports in Otolaryngology, Vol. 2014, p. 1.


A rare angiosarcoma: retiform haemangioendothelioma

  • F O'Duffy (a1), C Timon (a1) and M Toner (a2)
  • DOI:
  • Published online: 05 September 2011

We report the case of a rare angiosarcoma, retiform haemangioendothelioma, in an 18-year-old young man, which presented as a recurrent ulcerating lesion of the left pinna.


Case report and literature review of retiform haemangioendothelioma. This is a low grade angiosarcoma with a high local recurrence rate and low metastasis rate, and was first described in 1994 by Calonje et al.


This patient represents only the third report of lymph node metastasis in a case of retiform haemangioendothelioma. To date, 31 cases of the tumour have been reported. Histological diagnosis of this group of vascular neoplasms can be challenging, as their histopathological appearance is intermediate between haemangioma and angiosarcoma.


Surgical excision remains the primary treatment modality, with adjuvant radiotherapy recommended in patients with large tumour size, local recurrence and lymph node metastasis, as seen in this case.

Corresponding author
Address for correspondence: Mr Fergal O'Duffy, Royal Victoria Hospital, Adelaide Rd, Dublin 2, Ireland Fax: +353 14900643 E-mail:
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1E Calonje , CD Fletcher , E Wilson-Jones , J Rosai . Retiform haemangioendothelioma. A distinctive form of low-grade angiosarcoma delineated in a series of 15 cases. Am J Surg Pathol 1994;18:115–25

2D Tan , W Kraybill , RT Cheney , T Khoury . Retiform haemangioendothelioma: a case report and review of literature. J Cutan Pathol 2005;32:634–7

3B Bhutoria , A Konar , S Chakrabarti , S Das . Retiform hemangioendothelioma with lymph node metastasis: a rare entity. Indian J Dermatol Venereol Leprol 2009;75:60–2

4D Duke , AM Dvorak , T Harris , LM Cohen . Multiple retiform haemangioendotheliomias. A low-grade angiosarcoma. Am J Dermatopathol 1996;18:606–10

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The Journal of Laryngology & Otology
  • ISSN: 0022-2151
  • EISSN: 1748-5460
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