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The first reported treatment of Nager syndrome associated hearing loss with bone-anchored hearing aids: case report

Published online by Cambridge University Press:  12 October 2011

G P Davies  and
I J M Johnson
G P Davies*
Affiliation:
Newcastle University Medical School, Newcastle upon Tyne, UK
I J M Johnson
Affiliation:
BAHA Programme, Freeman Hospital, Newcastle upon Tyne, UK
*
Address for correspondence: Dr Gareth Peter Davies, Tudor Lodge, Brookfield Road, Churchdown, Gloucester GL3 2PF, UK Fax: +44 (0)1452 617 135 E-mail: g.p.davies1@ncl.ac.uk
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Abstract

Objective:

To report the first case of treatment of Nager syndrome associated conductive hearing loss with bone-anchored hearing aids, in a three-year-old boy.

Method:

Clinical case report and current literature review regarding the use of bone-anchored hearing aids in the treatment of conductive hearing loss in children.

Results:

A three year eight month old boy with Nager syndrome was successfully treated for conductive hearing loss using bilateral bone-anchored hearing aids.

Conclusion:

This is the first case report of the use of bone-anchored hearing aids to treat Nager syndrome associated conductive hearing loss. Treatment was safe and successful in this case.

Keywords

Acrofacial Dysostosis, Nager TypeBone-Anchored Hearing AidHearing Loss, Conductive
Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 126 , Issue 1 , January 2012 , pp. 76 - 78
Copyright
Copyright © JLO (1984) Limited 2011

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References

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