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An extremely rare clinical entity: congenitally corrected transposition with situs ınversus and single coronary artery presented with complete atrioventricular block in a young man

Part of: Cardiac Morphology

Published online by Cambridge University Press:  12 February 2018

Omer Faruk Cirakoglu Open the ORCID record for Omer Faruk Cirakoglu [Opens in a new window] ,
Ali Bayraktar  and
Muhammet Rasit Sayin
Omer Faruk Cirakoglu*
Affiliation:
Department of Cardiology, Trabzon Ahi Evren Training and Research Hospital, University of Health Science, Trabzon, Turkey
Ali Bayraktar
Affiliation:
Department of Cardiology, Trabzon Ahi Evren Training and Research Hospital, University of Health Science, Trabzon, Turkey
Muhammet Rasit Sayin
Affiliation:
Department of Cardiology, Trabzon Ahi Evren Training and Research Hospital, University of Health Science, Trabzon, Turkey
*
Author for correspondence: O. F. Cirakoglu, MD, Kardiyoloji Anabilim Dali, Ahi Evren Kalp ve Damar Cerrahisi EAH, Saglik Bilimleri Universitesi, Soguksu Vatan St. No: 9, 61040 Trabzon, Turkey. Tel: +90 462 231 04 64; Fax: +90 462 231 04 83; E-mail: omerfcirakoglu@hotmail.com
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Abstract

Congenitally corrected transposition of the great arteries is a rare form of CHD. Situs inversus is a much less common variant of a congenitally corrected transposition of the great arteries. In rare cases, transposition events may be accompanied by various cardiac anomalies. However, situs inversus patients with congenitally corrected transposition, single coronary artery anomaly, and atrioventricular block together have not been reported previously. This combination of abnormalities is presented as a first in the literature.

Keywords

Congenitally corrected transpositionsitus inversussingle coronary anomalyatrioventricular block
Type
Brief Report
Information
Cardiology in the Young , Volume 28 , Issue 5 , May 2018 , pp. 759 - 761
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Copyright
© Cambridge University Press 2018 

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References

1. Feingold, B, O’Sullivan, B, del Nido, P, et al. Situs inversus totalis and corrected transposition of the great arteries [I,D,D] in association with a previously unreported vascular ring. Pediatr Cardiol. 2001; 22: 338–342.Google Scholar
2. Ismat, FA, Baldwin, HS, Karl, TR, et al. Coronary anatomy in congenitally corrected transposition of the great arteries. Int J Cardiol 2002; 86: 207–216.Google Scholar
3. Shenthar, J, Rai, MK, Walia, R, et al. Transvenous permanent pacemaker implantation in dextrocardia: technique, challenges, outcome, and a brief review of literature. Europace. 2014; 16: 1327–1333.Google Scholar
4. Huhta, JC, Maloney, JD, Ritter, DG. Complete atrioventricular block in patients with atrioventricular discordance. Circulation. 1983; 67: 1374–1377.Google Scholar
5. Walmsley, T. Transposition of the ventricles and arterial stems. J Anat 1931; 65: 528–540.Google Scholar
6. Torgensen, J. Genic factors in visceral asymmetry in the development and pathological changes of the lungs, heart and abdominal organs. Arch Pathol 1949; 47: 566–593.Google Scholar
7. Lipton, MJ, Barry, WH, Obrez, I, et al. Isolated single coronary artery: diagnosis, angiographic classification, and clinical significance. Radiology. 1979; 130: 39–47.Google Scholar
8. Wester, JP, Ernst, JPMG, Mast, EG, et al. Coronary angioplasty in a patient with situs inversus totalis and a single coronary artery. Cathet Cardiovasc Diagn 1994; 31: 304–308.Google Scholar
9. Pott, C, Brar, R, Valderrabano, M. Implant of a biventricular pacemaker in a patient with dextrocardia and persistent left superior vena cava. Pacing Clin Electrophysiol 2006; 29: 921–922.Google Scholar
10. Kuwata, S, Yoneyama, K, Izumo, M, et al. A rare adult case of corrected transposition of the great vessels with situs inversus with a single coronary artery and an atrial septal defect. Int J Cardiol 2013; 168: e91–e93.Google Scholar