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The Congenital Heart Surgeons’ Society Registry of Anomalous Aortic Origin of a Coronary Artery: an update*

Published online by Cambridge University Press:  16 December 2015

Julie A. Brothers ,
J. William Gaynor ,
Jeffrey P. Jacobs ,
Jeffrey A. Poynter  and
Marshall L. Jacobs
Julie A. Brothers*
Affiliation:
Division of Cardiology, The Children’s Hospital of Philadelphia, Perelman School of Medicine, University of Pennsylvania, Philadelphia, Pennsylvania, United States of America
J. William Gaynor
Affiliation:
Department of Cardiothoracic Surgery, The Children’s Hospital of Philadelphia, Perelman School of Medicine, University of Pennsylvania, Philadelphia, Pennsylvania, United States of America
Jeffrey P. Jacobs
Affiliation:
Division of Cardiovascular Surgery, Department of Surgery, Johns Hopkins All Children’s Heart Institute, All Children’s Hospital and Florida Hospital for Children, Saint Petersburg, Tampa, Orlando, Florida, United States of America Division of Cardiac Surgery, Department of Surgery, Johns Hopkins University, Baltimore, Maryland, United States of America
Jeffrey A. Poynter
Affiliation:
Indiana University School of Medicine, United States of America
Marshall L. Jacobs
Affiliation:
Division of Cardiovascular Surgery, Department of Surgery, Johns Hopkins All Children’s Heart Institute, All Children’s Hospital and Florida Hospital for Children, Saint Petersburg, Tampa, Orlando, Florida, United States of America Division of Cardiac Surgery, Department of Surgery, Johns Hopkins University, Baltimore, Maryland, United States of America
*
Correspondence to: Dr J. A. Brothers, MD, The Children’s Hospital of Philadelphia, Division of Cardiology, 3401 Civic Center Boulevard, 8NW Room 75, Philadelphia, PA 19104, United States of America. Tel: 215-590-1804; Fax: 267-426-9800; E-mail: brothersj@email.chop.edu
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Abstract

The anomalous aortic origin of a coronary artery from the wrong sinus of Valsalva with an interarterial, intramural, and/or intraconal course is a relatively rare congenital defect of the heart that may be associated with an increased risk of ischaemia of the myocardium and sudden death, notably in children and young adults. Data are limited regarding stratification of risk and long-term outcomes of these patients. In 2009, the Anomalous Coronary Artery Working Group formed the Congenital Heart Surgeons’ Society Registry of Anomalous Aortic Origin of a Coronary Artery to obtain information on large numbers of young patients with anomalous aortic origin of a coronary artery with the goal to better understand the natural and surgical history of this anomaly as well as to develop evidence-based treatment and management guidelines. In this report, we describe the data we have collected from the registry and the current state of the registry.

Keywords

Congenital cardiac diseasepaediatric cardiac diseaseinterarterial coronary arteryintramural coronary arteryintraconal coronary artery
Type
Original Articles
Information
Cardiology in the Young , Volume 25 , Issue 8: HeartWeek 2015 , December 2015 , pp. 1567 - 1571
Copyright
© Cambridge University Press 2015 

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Footnotes

*

Presented at the Johns Hopkins All Children’s Heart Institute’s 15th Annual International Symposium on Congenital Heart Disease, Saint Petersburg, Florida, United States of America, from Friday, 6 February 2015, to Monday, 9 February 2015.

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