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Dissecting aneurysm of the pulmonary arteries—an unusual complication of congenital heart disease

  • Thomas M. Farrell (a1), Carol M. Cottrill (a1), William N. O'Connor (a1), Dede Boucher (a1) and Jacqueline A. Noonan (a1)...

Dissection of a pulmonary arterial aneurysm due to underlying pulmonary hypertension from congenital heart disease is uniformly fatal, but fortunately rare. Two such cases are presented, along with review of 24 other known cases published in the literature. Clinical presentation, guidelines tomanagement, and possible surgical intervention in the acutely dissecting patient are discussed.

Corresponding author
Dr. Carol M. Cottrill, Department of Pediatrics, University of Kentucky College of Medicine, Kentucky Clinic, Lexington, KY 40536-0284, USA. Tel. (606) 233-5494.
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Cardiology in the Young
  • ISSN: 1047-9511
  • EISSN: 1467-1107
  • URL: /core/journals/cardiology-in-the-young
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