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Hepatocellular carcinoma in the adult Fontan patient

  • Michael R. Conroy (a1) and Tabitha G. Moe (a1)

In this study, we describe the case of a 36-year-old woman who was diagnosed with hepatocellular carcinoma on a background of Fontan procedure for tricuspid atresia. She had worsening heart failure in the months before presentation, and early investigations noted derangement in liver enzymes and hepatomegaly. Liver biopsy confirmed a hepatocellular carcinoma. Hepatocellular carcinoma is a rare but recognised consequence of cardiac cirrhosis in Fontan patients.

Corresponding author
Correspondence to: Dr T. Moe, Department of Cardiology, Mayo Clinic, Scottsdale, AZ 85054, United States of America. Tel: 480 515 6296; Fax: 602 933 4166; E-mail:
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Cardiology in the Young
  • ISSN: 1047-9511
  • EISSN: 1467-1107
  • URL: /core/journals/cardiology-in-the-young
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