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Longer-term issues for young adults with hypoplastic left heart syndrome: contraception, pregnancy, transition, transfer, counselling, and re-operation

Published online by Cambridge University Press:  13 December 2011

Sameh M. Said ,
Joseph A. Dearani ,
Candice K. Silversides ,
Richard M. Martinez  and
David B. Drajpuch
Sameh M. Said
Affiliation:
Department of Cardiac Surgery, Mayo Clinic, Rochester, Minnesota, Canada
Joseph A. Dearani
Affiliation:
Department of Cardiac Surgery, Mayo Clinic, Rochester, Minnesota, Canada
Candice K. Silversides
Affiliation:
Division of Cardiology, Mount Sinai and Toronto General Hospitals, Toronto, Ontario, Canada
Richard M. Martinez
Affiliation:
Division of Pediatric Cardiology, The Congenital Heart Institute of Florida (CHIF), All Children's Hospital, University of South Florida College of Medicine, Saint Petersburg, Florida, United States of America
David B. Drajpuch*
Affiliation:
Department of Cardiac Nursing, Children's Hospital of Philadelphia, Philadelphia, Pennsylvania, United States of America
*
Correspondence to: D. B. Drajpuch, MSN CRNP, Children's Hospital of Philadelphia, 12NW10, 34th Street and Civic Center Boulevard, Philadelphia, Pennsylvania 19104, United States of America. Tel: +1 215 590 2708; Fax: +1 215 590 2715; E-mail: drajpuchd@email.chop.edu
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Abstract

Hypoplastic left heart syndrome remained a largely untreated lesion until the 1980s. In the current era, 75–80% of patients who are managed at “centres of excellence” can be expected to survive into young adulthood after staged palliation. This improved survival has led to an emerging population of patients now entering adulthood with a new set of concerns. We discuss the realised and potential issues that will be faced by these patients, including family planning, transition, and re-operation.

Keywords

Fontanadult congenital heart diseasefamily planningsurgery
Type
Original Article
Information
Cardiology in the Young , Volume 21 , Issue S2: A Holistic Approach to Hypoplastic Left Heart Syndrome and other evolving challenges in Pediatric and Congenital Cardiac Disease , 13 December 2011 , pp. 93 - 100
Copyright
Copyright © Cambridge University Press 2011

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