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Primary-care management of patients with congenital anomalies of the coronary arteries*

Published online by Cambridge University Press:  16 December 2015

Jeffrey R. Boris*
Affiliation:
Children’s Hospital of Philadelphia, Perelman School of Medicine, University of Pennsylvania, Philadelphia, Pennsylvania, United States of America
Julie A. Brothers
Affiliation:
Children’s Hospital of Philadelphia, Perelman School of Medicine, University of Pennsylvania, Philadelphia, Pennsylvania, United States of America
*
Correspondence to: Dr J. R. Boris, MD, Division of Cardiology, Children’s Hospital of Philadelphia, 3401 Civic Center Boulevard, Philadelphia, PA 19104, United States of America. Tel: 215-590-3180; Fax: 267-426-5324; E-mail: borisj@email.chop.edu

Abstract

Congenital anomalies of the coronary arteries, although uncommon, have the potential to cause serious myocardial damage, ischaemic cardiomyopathy, and sudden cardiac death. This article summarises aspects of care for these patients in the outpatient setting, including clinical history and physical examination findings, ancillary testing, decision-making regarding the need for surgical intervention, and recommendations for physical activity. Although there are limited data regarding some of these recommendations, it is hoped that these can be used as an initial benchmark against which further data will lead to a more evidence-based approach.

Type
Original Articles
Copyright
© Cambridge University Press 2015 

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Footnotes

*

Presented at the Johns Hopkins All Children’s Heart Institute’s 15th Annual International Symposium on Congenital Heart Disease, Saint Petersburg, Florida, United States of America, from Friday, 6 February, 2015 to Monday, 9 February, 2015.

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