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A rare case of pulmonary lymphangiectasia associated with CHD

Part of: Advanced Imaging

Published online by Cambridge University Press:  17 June 2021

Cláudio Henriques Open the ORCID record for Cláudio Henriques [Opens in a new window] ,
Ana Lai ,
Helena Andrade ,
Raquel Pina ,
António Marinho-da-Silva Open the ORCID record for António Marinho-da-Silva [Opens in a new window]  and
António Pires
Cláudio Henriques*
Affiliation:
Paediatric Cardiology Department, Paediatric Hospital, Coimbra, Portugal
Ana Lai
Affiliation:
Anatomical Pathology Department, University Hospital, Coimbra, Portugal
Helena Andrade
Affiliation:
Paediatric Cardiology Department, Paediatric Hospital, Coimbra, Portugal
Raquel Pina
Affiliation:
Anatomical Pathology Department, University Hospital, Coimbra, Portugal
António Marinho-da-Silva
Affiliation:
Paediatric Cardiology Department, Paediatric Hospital, Coimbra, Portugal
António Pires
Affiliation:
Paediatric Cardiology Department, Paediatric Hospital, Coimbra, Portugal
*
Author for correspondence: Dr. Cláudio Henriques, Hospital Pediátrico de Coimbra, Avenida Afonso Romão, Coimbra, 3000-602, Portugal. Tel: +351239488700. E-mail: claudiojhenriques@gmail.com
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Abstract

CHD may, at times, occur in the framework of other rare pathologies. These, having similar clinical manifestations, present a diagnostic dilemma for the clinician.

The authors present the case of an infant with non-syndromic complete atrioventricular septal defect, whose post-operative period was surprisingly complicated by progressive pulmonary hypertension. Despite intensive care, the infant ultimately died. The diagnosis of unilateral primary pulmonary lymphangiectasia was only possible post mortem.

Keywords

Primary pulmonary lymphangiectasiapulmonary venous connectioncomplete atrioventricular septal defectpulmonary hypertension
Type
Brief Report
Information
Cardiology in the Young , Volume 32 , Issue 1 , January 2022 , pp. 132 - 134
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Copyright
© The Author(s), 2021. Published by Cambridge University Press

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