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Right aortic arch with a unique branching pattern, coarctation of the aorta, and vascular ring: a management conundrum

Published online by Cambridge University Press:  16 October 2025

Gabriel N. Bahrami Open the ORCID record for Gabriel N. Bahrami [Opens in a new window] ,
Yumna Maredia ,
Harinder R. Singh ,
Daniel Nento  and
Arpit Agarwal
Gabriel N. Bahrami*
Affiliation:
Division of Pediatric Cardiology at University Hospitals Rainbow Babies & Children’s Hospital, Cleveland, OH, USA
Yumna Maredia
Affiliation:
University of the Incarnate Word School of Osteopathic Medicine, San Antonio, TX, USA
Harinder R. Singh
Affiliation:
Division of Pediatric Cardiology at University Hospitals Rainbow Babies & Children’s Hospital, Cleveland, OH, USA
Daniel Nento
Affiliation:
Division of Pediatric Cardiology at University Hospitals Rainbow Babies & Children’s Hospital, Cleveland, OH, USA
Arpit Agarwal
Affiliation:
Division of Pediatric Cardiology at University Hospitals Rainbow Babies & Children’s Hospital, Cleveland, OH, USA
*
Corresponding author: Gabriel N Bahrami; Email: gabriel.bahrami@uhhospitals.org
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Abstract

The combination of a right aortic arch with a vascular ring and coarctation of the aorta is a rare association, presenting a unique management challenge for the primary team. A thorough literature review revealed only seven published case reports, with three cases reported in the neonatal period with similar anatomy. This distinctive anatomy inspires inquiry into the development of coarctation in the context of a right aortic arch and vascular ring, as well as the best approach to surgical management. We encountered a similar case in a neonate with a combination of these malformations and a unique aortic arch branching pattern. Cardiac CT was instrumental in the diagnosis and surgical planning. This article reviews the variations in anatomy, clinical presentation, imaging findings, and management challenges encountered in the reported cases. This comprehensive review aims to assist the primary team in making informed decisions when treating these complex patients.

Keywords

Right aortic archcoarctation of the aortavascular ringcardiac CTsurgical management

Information

Type
Review
Information
Cardiology in the Young , First View , pp. 1 - 5
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Copyright
© The Author(s), 2025. Published by Cambridge University Press

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