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Right ventricle-dependent coronary circulation diagnosed by non-invasive ferumoxytol-enhanced 4D cardiac magnetic resonance angiography in pulmonary atresia with intact ventricular septum

Published online by Cambridge University Press:  28 September 2022

Joshua Rezkalla Open the ORCID record for Joshua Rezkalla [Opens in a new window] ,
Stephanie A. Raymundo Open the ORCID record for Stephanie A. Raymundo [Opens in a new window]  and
Pierangelo Renella
Joshua Rezkalla
Affiliation:
Department of Cardiovascular Medicine, Mayo Clinic, Rochester, MN, USA
Stephanie A. Raymundo*
Affiliation:
Division of Pediatric Cardiology, Department of Pediatrics, Helen Devos Children’s Hospital, Grand Rapids, MI 49503, USA
Pierangelo Renella
Affiliation:
Department of Radiology, David Geffen School of Medicine at UCLA, Los Angeles, CA, USA Department of Pediatrics, UC-Irvine School of Medicine, Irvine, CA, USA Division of Pediatric Cardiology, CHOC Children’s Hospital, Orange, CA, USA
*
Author for correspondence: Stephanie Raymundo, MD, Helen Devos Children’s Hospital Congenital Heart Center, 25 Michigan Street NE #4200, Grand Rapids, MI 49503, USA. Email: stephanie.raymundo@helendevoschildrens.org
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Abstract

Pulmonary atresia with intact ventricular septum is a complex cyanotic congenital heart lesion with the potential for myocardial ischaemia due to the presence of coronary artery anomalies. We present a case of a two-day-old baby with postnatal diagnosis of pulmonary atresia with intact ventricular septum in whom non-invasive ferumoxytol-enhanced 4D cardiac magnetic resonance angiography was used for the assessment of coronary artery anatomy.

Keywords

Cardiac MRIcardiac magnetic resonance angiographyferumoxytolCHDpulmonary atresia with intact ventricular septumcoronary artery fistula

Information

Type
Brief Report
Information
Cardiology in the Young , Volume 33 , Issue 6 , June 2023 , pp. 1001 - 1003
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Copyright
© The Author(s), 2022. Published by Cambridge University Press

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References

Chikkabyrappa, SM, Loomba, RS, Tretter, JT. Pulmonary atresia with an intact ventricular septum: preoperative physiology, imaging, and management. Semin Cardiothorac Vasc Anesth. 2018; 22: 245–255. DOI 10.1177/1089253218756757.CrossRefGoogle ScholarPubMed
Hasan, BS, Bautista-Hernandez, V, McElhinney, DB, et al. Outcomes of transcatheter approach for initial treatment of pulmonary atresia with intact ventricular septum. Catheter Cardiovasc Interv. 2013; 81: 111–118. DOI 10.1002/ccd.24288.CrossRefGoogle ScholarPubMed
Gleich, S, Latham, GJ, Joffe, D, Ross, FJ. Perioperative and anesthetic considerations in pulmonary atresia with intact ventricular septum. Semin Cardiothorac Vasc Anesth. 2018; 22: 256–264. DOI 10.1177/1089253217737180.CrossRefGoogle ScholarPubMed
Loomba, RS, Pelech, AN. Aortic perfusion score for pulmonary atresia with intact ventricular septum: an antegrade coronary perfusion scoring system that is predictive of need for transplant and mortality. Congenit Heart Dis. 2018; 13: 92–97. DOI 10.1111/chd.12510.CrossRefGoogle ScholarPubMed
Saltik, L, Bayrak, F, Guneysu, T, Sevinc, D, Oztunc, F, Degertekin, M. RV-dependent coronary circulation demonstrated with 64-slice computed tomography. Eur Heart J 2008; 29: 1018–1018. DOI 10.1093/eurheartj/ehm514.CrossRefGoogle Scholar