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Systemic hypertension in an infant with unrepaired tetralogy of Fallot: case report

  • Michael Khoury (a1), Michael Kallile (a2), Joseph May (a2) and Rajesh Punn (a2)

Patients with severe right ventricular outflow tract obstruction in tetralogy of Fallot typically have right-to-left shunting, resulting in low pulmonary blood flow and cyanosis. Here we present the case of an infant with tetralogy of Fallot and severe pulmonary valve stenosis, complicated by systemic hypertension, the presence of which altered flow dynamics and possibly prevented cyanosis.

Corresponding author
Correspondence to: Dr R. Punn, MD, Division of Pediatric Cardiology, Lucile Packard Children's Hospital, 750 Welch Road, Suite no. 305, Palo Alto, CA 94304, United States of America. Tel: +1 650 498 4563; Fax: +1 650 725 8343; E-mail:
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4. MD Pettersen , W Du , ME Skeens , RA Humes . Regression equations for calculation of z scores of cardiac structures in a large cohort of healthy infants, children, and adolescents: an echocardiographic study. J Am Soc Echocardiogr 2008; 21: 922934.

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Cardiology in the Young
  • ISSN: 1047-9511
  • EISSN: 1467-1107
  • URL: /core/journals/cardiology-in-the-young
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