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Unguarded tricuspid valvar orifice in the fetus

Published online by Cambridge University Press:  21 January 2005

Kenny K. Wong ,
Duncan I. Farquharson  and
Walter J. Duncan
Kenny K. Wong
Affiliation:
Division of Pediatric Cardiology, British Columbia Children’s and Women’s Hospitals, Vancouver, British Columbia, Canada
Duncan I. Farquharson
Affiliation:
Division of Maternal Fetal Medicine, British Columbia Children’s and Women’s Hospitals, Vancouver, British Columbia, Canada
Walter J. Duncan
Affiliation:
Division of Pediatric Cardiology, British Columbia Children’s and Women’s Hospitals, Vancouver, British Columbia, Canada
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Abstract

The unguarded tricuspid valve is uncommon. We describe herein a fetus with a grossly dilated right ventricle and atrium, with severe tricuspid and pulmonary valvar regurgitation. The right ventricle was akinetic, and no tricuspid tissue or valvar apparatus was identified. Colour Doppler showed a highly unusual retrograde flow of blood through the right heart. The pregnancy was terminated, and necropsy examination confirmed the gross dilation of the right heart chambers, with severely dysplastic valvar tissue at the right atrioventricular junction effectively giving an unguarded orifice. There was no valvar displacement, and the left heart was normal. The fetus had a normal karyotype, albeit with absent kidneys.

Keywords

Dysplastic tricuspid valvefetal echocardiographyright-to-left shunting
Type
Brief Report
Information
Cardiology in the Young , Volume 14 , Issue 5 , October 2004 , pp. 557 - 559
Copyright
© 2004 Cambridge University Press

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