Hostname: page-component-5db58dd55d-8lnk4 Total loading time: 0 Render date: 2026-05-31T17:43:56.261Z Has data issue: false hasContentIssue false
  • English
  • Français

Isolated congenital stapes suprastructure fixation

Published online by Cambridge University Press:  29 June 2007

V. Nandapalan  and
M. Tos
V. Nandapalan*
Affiliation:
Department of Otolaryngology Gentafte University HospitalCopenhagen, Denmark Department of Otolaryngology, University Hospital Aintree, Liverpool, UK.
M. Tos
Affiliation:
Department of Otolaryngology Gentafte University HospitalCopenhagen, Denmark
*
Address for correspondence: V. Nandapalan, 6 Pinnington Road, Whiston, Liverpool L35 3TY.
Get access Rights & Permissions [Opens in a new window]

Abstract

Isolated congenital anomalies of the ossicles are rare. The majority of cases of congenital conductive hearing loss secondary to middle-ear anomalies have other associated defects, such as atresia, microtia and craniofacial deformities.

We present a rare case of isolated congenital stapes suprastructure fixation, where a monocrural stapes with a mobile footplate was attached to the promontory by bony synostosis. There was no stapedius muscle nor pyramidal process. The incus and malleus were of normal configuration. Mobilization of the stapes from the promontory resulted in improvement in hearing. We believe this is the first reported case of such an abnormality. A review of the world literature of isolated stapes suprastructure ankylosis and the classifications of minor congenital anomalies are discussed.

Keywords

StapesSynostosisStapes mobilization

Information

Type
Main Articles
Information
The Journal of Laryngology & Otology , Volume 113 , Issue 9 , September 1999 , pp. 798 - 802
Copyright
Copyright © JLO (1984) Limited 1999

Access options

Get access to the full version of this content by using one of the access options below. (Log in options will check for institutional or personal access. Content may require purchase if you do not have access.)

Article purchase

Temporarily unavailable

References

Arslan, M., Giacomelli, F. (1963) Considerations cliniques sur l'ankylose stapedio-vestibulaire congenitale. Annales d'Oto Laryngologie et de chirurgie de la Face (Paris) 80: 13–28.Google Scholar
Charachon, R., Barthez, M. P., Lavieille, J. P. (1994) Les malformations mineures de la chaine ossiculaire. Annales d'Oto Laryngologie et de chirurgie de la Face (Paris) 111: 69–74.Google Scholar
Cremers, C. W. R. J., Hoogland, G. A. (1986) Congenital stapes ankylosis by elongation of the pyramidal eminence communication. Annals of Otology, Rhinology and Laryngology 95: 167–168.CrossRefGoogle ScholarPubMed
Cremers, C. W. R. J., Teunissen, E. (1991) A classification of minor congenital ear anomalies and short and long term results of surgery in 104 ears. In Long Term Results and Indications in Otology and Otoneurosurgery. Proceedings of the Politzer Society Conferences in Ibiza, 1989 and Courchevel 1990. Edited by Charachon, R. and Garcia-Ibanez, E., Kugler Publications, pp 11–12.Google Scholar
Funasaka, S. (1979) Congenital ossicular anomalies without malformations of the external ear. Archives of Otorhinolaryngology 224: 231–240.CrossRefGoogle ScholarPubMed
Gerhardt, H. J., Otto, H. D. (1970) Steigbugelmissbildungen. Acta Otolaryngologica (Stockholm) 70: 35–44.CrossRefGoogle Scholar
Grant, W. E., Grant, W. J. (1991) Stapedius tendon ossification: A rare cause of congenital conductive hearing loss. Journal of Laryngology and Otology 105: 763–764.CrossRefGoogle ScholarPubMed
Hanson, J. R., Anson, B. J., Strickland, E. M. (1962) Branchial sources of the auditory ossicles in man. Part II: Observations of embryonic stages from 7 mm to 28 mm (CR length). Archives of Otolaryngology 76: 20–35.Google Scholar
Henner, R., Buckingham, R. A. (1956) Recognition and surgical treatment of congenital ossicular defects. Laryngoscope 66: 526–539.CrossRefGoogle ScholarPubMed
Henner, R. (1960) Congenital middle ear malformations. Archives of Otolaryngology 71: 454–458.CrossRefGoogle ScholarPubMed
Hough, J. V. D. (1958) Malformations and anatomical variations seen in the middle ear during the operation for mobilization of stapes. Laryngoscope 68: 1337–1379.CrossRefGoogle ScholarPubMed
Kinsella, J. B., Kerr, A. G. (1993) Familial stapes superstructure fixation. Journal of Laryngology and Otology 107: 36–38.CrossRefGoogle ScholarPubMed
Manolidis, L., Daniilidis, I., Moser, M. (1972) Uber isolierte MiBbildungen des Mittelohres. HNO (Berlin) 70: 176–179.Google Scholar
Martin, C. H., Martin, H., Prades, J. M., Perron, X., Garban, T. H. (1986) Trepanation labyrinthique et malformation congenitale. Annales d'Oto Laryngologie et de chirurgie de la Face (Paris) 103: 525–545.Google Scholar
Meuser, W. (1977) Schalleitungsschwerhorigkeit durch verknocherte stapediussehnen. Laryngologie, Rhinologie, Otologie und ihre Grenzgebiete (Stuttgart) 56: 12–13.Google Scholar
Ombredanne, M. (1960) Chirurgie des surdites congenitales par malformations ossiculares de 10 nouveaux cas. Annales d'Oto Laryngologie et de chirurgie de la Face (Paris) 77: 423–449.Google Scholar
Ombredanne, M. (1964) Chirurgie des aplasies mineures. Ses resultats dans les grandes surdites congenitales par malformations ossiculaires. Annales d'Oto Laryngologie et de chirurgie de la Face (Paris) 8: 201–222.Google Scholar
Patel, K. N. (1972) Ossification of the stapedius tendon. Journal of Laryngology and Otology 86: 863–865.CrossRefGoogle ScholarPubMed
Plester, D. (1971) Congenital malformations of the middle ear. Acta Otolaryngologica (Belg) 25: 874–884.Google ScholarPubMed
Podoshin, L., Fradis, M., Zisman, D. (1972) Congenital anomalies of the stapes. Archives of Otolaryngology 96: 254–255.CrossRefGoogle ScholarPubMed
Swartz, J. D., Glazer, A. U., Faerber, E. N., Capitanio, M. A., Popky, G. L. (1986) Congenital middle ear deafness: CT study. Radiology 159: 187–190.CrossRefGoogle ScholarPubMed
Schuknecht, H. F., Trupiano, S. (1957) Some interesting middle ear problems. Laryngoscope 67: 395–409.CrossRefGoogle ScholarPubMed
Teunissen, E., Cremers, C. W. R. J. (1990) Isolated congenital stapes ankylosis. Surgical findings and results in 32 ears and a review of the literature. Laryngoscope 100: 1331–1336.CrossRefGoogle Scholar