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Sweet's disease and profound, bilateral, sensorineural hearing loss

Published online by Cambridge University Press:  20 October 2009

S Cheng  and
M da Cruz
S Cheng*
Affiliation:
Department of Otolaryngology, Westmead Hospital, University of Sydney, New South Wales, Australia
M da Cruz
Affiliation:
Department of Otolaryngology, Westmead Hospital, University of Sydney, New South Wales, Australia
*
Address for correspondence: Prof Melville da Cruz, Department of Surgery, Westmead Hospital, Hawkesbury Road, Westmead, NSW, Australia 2145. Fax: +61 2 98937440 E-mail: melvilled@westgate.wh.usyd.edu.au
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Abstract

Objective:

We report a case of Sweet's disease associated with rapid, profound loss of hearing, against a background of progressive, bilateral, sensorineural hearing loss.

Results:

The clinical features were indistinguishable from those of immune-mediated inner ear disease. Establishment of a definitive diagnosis was a challenge due to the absence of a reliable diagnostic test. The patient was unresponsive to extensive immunosuppressive therapy and subsequently underwent cochlear implantation, with good hearing outcomes.

Conclusions:

Profound, bilateral, sensorineural hearing loss in the context of Sweet's disease may be related to the underlying immunological aetiology. Cochlear implantation can successfully restore hearing when immunotherapy fails.

Keywords

Sweet's DiseaseSensorineural hearing lossCochlear Implant

Information

Type
Clinical Records
Information
The Journal of Laryngology & Otology , Volume 124 , Issue 1 , January 2010 , pp. 105 - 107
Copyright
Copyright © JLO (1984) Limited 2009

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