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Echocardiography of hypoplastic left heart syndrome

Published online by Cambridge University Press:  13 December 2011

Thieu Nguyen ,
Michelle Miller ,
Javier Gonzalez ,
Katherine Nardell ,
James Galas ,
John B. John ,
Stan Timofeev ,
Rich Lambou ,
Kathryn Douglas  and
Gerald Marx
Thieu Nguyen*
Affiliation:
All Children's Hospital, Saint Petersburg, Florida, United States of America
Michelle Miller
Affiliation:
All Children's Hospital, Saint Petersburg, Florida, United States of America
Javier Gonzalez
Affiliation:
Pediatric Cardiology Associates/Pediatrix Medical Group, Saint Petersburg and Tampa, Florida, United States of America
Katherine Nardell
Affiliation:
All Children's Hospital, Saint Petersburg, Florida, United States of America
James Galas
Affiliation:
All Children's Hospital, Saint Petersburg, Florida, United States of America
John B. John
Affiliation:
All Children's Hospital, Saint Petersburg, Florida, United States of America Pediatric Cardiology Associates/Pediatrix Medical Group, Saint Petersburg and Tampa, Florida, United States of America
Stan Timofeev
Affiliation:
Department of Cardiology, University of Florida, Tampa, Florida, United States of America
Rich Lambou
Affiliation:
All Children's Hospital, Saint Petersburg, Florida, United States of America
Kathryn Douglas
Affiliation:
All Children's Hospital, Saint Petersburg, Florida, United States of America
Gerald Marx
Affiliation:
Department of Cardiology, Children's Hospital Boston, Boston, Massachusetts, United States of America
*
Correspondence to: Dr T. P. Nguyen, MD, All Children's Hospital – Heart Institute of Florida, 2nd Floor Outpatient Care Center, 601 5th Street South, Saint Petersburg, Florida 33701, United States of America. Tel: +1 727 767 3333; Fax: +1 727 767 8990; E-mail: Thieu.nguyen@allkids.org
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Abstract

Echocardiography is critical in the assessment of patients with hypoplastic left heart syndrome. Fundamental techniques and standardised approaches are useful when evaluating patients with hypoplastic left heart syndrome prenatally, after birth, and before the Norwood operation (Stage 1); after the Norwood operation, before and after the superior cavopulmonary anastomosis (Stage 2); before and after the Fontan operation (Stage 3); and for chronic surveillance after the Fontan operation. From foetal assessment to ongoing surveillance after the Fontan procedure, echocardiography remains the primary technique for cardiac monitoring in this growing population of children and adults.

Keywords

Hypoplastic left heart syndromeechocardiographycongenital cardiac disease

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References

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