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Haemodynamic consequences following closure of an Abernethy malformation in a patient following a total cavopulmonary shunt

Published online by Cambridge University Press:  21 February 2018

Deepa Sasikumar ,
Bijulal Sasidharan  and
Anoop Ayyappan
Deepa Sasikumar
Affiliation:
Department of Cardiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, India
Bijulal Sasidharan*
Affiliation:
Department of Cardiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, India
Anoop Ayyappan
Affiliation:
Department of Imaging Sciences and Interventional Radiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, India
*
Author for correspondence: Bijulal Sasidharan, Department of Cardiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, 695011, India. Tel: +91 94465 90185; Fax: 91 471 2446433; E-mail: drbijulalsasidharan@gmail.com
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Abstract

A 17-year-old girl with situs ambiguous, hypoplastic right ventricle with a large ventricular septal defect, and severe pulmonary stenosis had undergone Kawashima operation 10 years back. She had significant desaturation because of a large Abernethy malformation, with reverse shunting from the inferior caval vein to the portal vein. It was closed with a vascular plug, with improvement in oxygen saturation. She developed extensive inferior caval vein thrombus following the procedure, which was managed conservatively by anti-coagulation.

Keywords

AbernethyheterotaxyKawashima

Information

Type
Brief Report
Information
Cardiology in the Young , Volume 28 , Issue 5 , May 2018 , pp. 768 - 770
Copyright
© Cambridge University Press 2018 

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References

1. Morgan, G, Superina, R. Congenital absence of the portal vein: two cases and a proposed classification system for portasystemic vascular anomalies. J Pediatr Surg 1999; 29: 1239–1241.Google Scholar
2. Kothari, SS. Non-cardiac issues in patients with heterotaxy syndrome. Ann Pediatr Cardiol 2014; 7: 187–192.Google Scholar
3. Ratnasamy, C, Kubegov, A, Swaminathan, S. Cardiac anomalies in the setting of the Abernethy malformation of the portal vein. Cardiol Young 2007; 17: 212–214.CrossRefGoogle ScholarPubMed
4. Doraiswamy, V, Sivakumar, K. Impact of Abernathy malformation on pulmonary circulatory hemodynamics in a univentricular heart. Ann Pediatr Cardiol 2017; 10: 90–91.Google Scholar
5. Knirsch, W, Benz, DC, Bühr, P, et al. Catheter interventional treatment of congenital portosystemic venous shunts in childhood. Catheter Cardiovasc Interv. 2016; 87: 1281–1292.Google Scholar

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