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Spontaneous Spinal Epidural Hematoma in a Child with Hemophilia B

Published online by Cambridge University Press:  02 December 2014

Erica F. Bisson ,
Travis Dumont  and
Bruce Tranmer
Erica F. Bisson
Affiliation:
Department of Neurosurgery, University of Vermont College of Medicine, Berlington, Vermont, USA
Travis Dumont
Affiliation:
Department of Neurosurgery, University of Vermont College of Medicine, Berlington, Vermont, USA
Bruce Tranmer
Affiliation:
Division of Neurosurgery, University of Vermont College of Medicine, Berlington, Vermont, USA
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Central nervous system hemorrhage is an uncommon and potentially devastating event in hemophiliacs, with an incidence of 2-8%. Intraspinal hematomas account for 8.5% of CNS hemorrhages in patients with factor VIII or IX deficiencies. Although most reported cases in this population are secondary to trauma, there are a few reports of spontaneous hemorrhage. We present a case of spontaneous spinal epidural hematoma (SSEH) in a child with Hemophilia B, factor IX deficiency, and review the relevant management strategies.

Type
Peer Reviewed Letter
Information
Canadian Journal of Neurological Sciences , Volume 34 , Issue 4 , November 2007 , pp. 488 - 490
Copyright
Copyright © The Canadian Journal of Neurological 2007

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