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Chapter 18 - Epilepsy Syndromes

from Part III - Specific Conditions

Published online by Cambridge University Press:  27 September 2025

Neville M. Jadeja
Affiliation:
UMass Chan Medical School
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Summary

Epilepsy syndromes (electroclinical syndromes) are well-recognized groupings of clinical (seizure types) and EEG features that occur together. Each syndrome typically shares a common age of onset, deficits (intellectual dysfunction), treatment and prognosis. Syndromes are classified based on their onset, epilepsy type (focal, generalized, or mixed) and development of epileptic encephalopathy (disorder in which epileptic activity contributes to severe impairments in cognition and behavior). Relatively benign syndromes are typically associated with focal, generalized tonic-clonic (GTC), typical absences and myoclonic seizures. Epileptic encephalopathies are typically associated with atonic, tonic, atypical absences, and epileptic spasms in addition to the other seizure types. [106 words/729 characters]

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References

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  • Epilepsy Syndromes
  • Neville M. Jadeja, UMass Chan Medical School
  • Book: How to Read an EEG
  • Online publication: 27 September 2025
  • Chapter DOI: https://doi.org/10.1017/9781009539210.022
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  • Epilepsy Syndromes
  • Neville M. Jadeja, UMass Chan Medical School
  • Book: How to Read an EEG
  • Online publication: 27 September 2025
  • Chapter DOI: https://doi.org/10.1017/9781009539210.022
Available formats
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Save book to Google Drive

To save content items to your account, please confirm that you agree to abide by our usage policies. If this is the first time you use this feature, you will be asked to authorise Cambridge Core to connect with your account. Find out more about saving content to Google Drive.

  • Epilepsy Syndromes
  • Neville M. Jadeja, UMass Chan Medical School
  • Book: How to Read an EEG
  • Online publication: 27 September 2025
  • Chapter DOI: https://doi.org/10.1017/9781009539210.022
Available formats
×