Book contents
- Frontmatter
- Contents
- List of contributors
- Preface
- Acknowledgment
- Section 1 Head and neck
- Case 1 Trilateral retinoblastoma
- Case 2 Fibromatosis colli
- Case 3 Craniopharyngioma
- Case 4 Labyrinthitis ossificans
- Case 5 Branchio-oto-renal syndrome
- Case 6 Medulloblastoma
- Case 7 Ectopic cervical thymus
- Case 8 X-linked adrenoleukodystrophy
- Case 9 Langerhans cell histiocytosis
- Case 10 PHACES syndrome (Posterior fossa malformations, Hemangiomas of the face, Arterial anomalies, Cardiovascular anomalies, Eye anomalies, and Sternal defects or supraumbilical raphe)
- Section 2 Thoracic imaging
- Section 3 Cardiac imaging
- Section 4 Vascular and interventional
- Section 5 Gastrointestinal imaging
- Section 6 Urinary imaging
- Section 7 Endocrine - reproductive imaging
- Section 8 Fetal imaging
- Section 9 Musculoskeletal imaging
- Index
- References
Case 9 - Langerhans cell histiocytosis
from Section 1 - Head and neck
Published online by Cambridge University Press: 05 June 2014
Book contents
- Frontmatter
- Contents
- List of contributors
- Preface
- Acknowledgment
- Section 1 Head and neck
- Case 1 Trilateral retinoblastoma
- Case 2 Fibromatosis colli
- Case 3 Craniopharyngioma
- Case 4 Labyrinthitis ossificans
- Case 5 Branchio-oto-renal syndrome
- Case 6 Medulloblastoma
- Case 7 Ectopic cervical thymus
- Case 8 X-linked adrenoleukodystrophy
- Case 9 Langerhans cell histiocytosis
- Case 10 PHACES syndrome (Posterior fossa malformations, Hemangiomas of the face, Arterial anomalies, Cardiovascular anomalies, Eye anomalies, and Sternal defects or supraumbilical raphe)
- Section 2 Thoracic imaging
- Section 3 Cardiac imaging
- Section 4 Vascular and interventional
- Section 5 Gastrointestinal imaging
- Section 6 Urinary imaging
- Section 7 Endocrine - reproductive imaging
- Section 8 Fetal imaging
- Section 9 Musculoskeletal imaging
- Index
- References
Summary
Imaging description
A 10-year-old boy presented with pain and soft tissue swelling of the left cheek. A CT scan demonstrated an extensive soft tissue mass centered in the left maxilla with associated cortical erosion of the left alveolar ridge and left maxillary sinus walls. Contralateral involvement of the right alveolar ridge and anterior maxillary sinus wall was also noted. Several teeth appeared to be “floating” within the maxilla. There was absence of adjacent soft tissue fat stranding (Fig. 9.1a–c).
A five-month-old infant presented with bi-parietal scalp swelling. CT of the head showed bi-parietal calvarial lytic lesions with associated soft tissue masses and a characteristic “beveled edge” appearance with greater destruction of the outer table of the calvarium relative to the inner table (Fig. 9.2a, b). On MRI, mixed T1 and T2 intensities and heterogeneous enhancement of the soft tissue mass was seen (Fig. 9.2c–e).
Langerhans cell histiocytosis (LCH) was confirmed pathologically in both cases.
Information
- Type
- Chapter
- Information
- Pearls and Pitfalls in Pediatric ImagingVariants and Other Difficult Diagnoses, pp. 25 - 29Publisher: Cambridge University PressPrint publication year: 2014
References
, , , et al. Langerhans’ cell histiocytosis: pathology, imaging and treatment of skeletal involvement. Pediatr Radiol 2005;35(2):103–15.CrossRefGoogle ScholarPubMed
, . Paediatric neuroradiological aspects of Langerhans cell histiocytosis. Neuroradiology 2008;50(1):85–92.CrossRefGoogle ScholarPubMed
, , , . Pediatric Hematology. Malden, Massachusetts: Blackwell Publishing, Inc., 2006.Google Scholar
, . Langerhans cell histiocytosis. In: , , , eds. Imaging of Bone Tumors and Tumor Like Conditions. Heidelberg: Springer, 2009; 447–59.CrossRefGoogle Scholar
, , . From the archives of the AFIP Langerhans cell histiocytosis of bone. Radiographics 1992;12(4):801–23.CrossRefGoogle Scholar
Accessibility standard: Unknown
Why this information is here
This section outlines the accessibility features of this content - including support for screen readers, full keyboard navigation and high-contrast display options. This may not be relevant for you.Accessibility Information
Accessibility compliance for the PDF of this chapter is currently unknown
and may be updated in the future.