Inner ear malformations, particularly incomplete partition type I, are well-recognised risk factors for cerebrospinal fluid leakage, which may result in recurrent meningitis.

We present a case series of three paediatric patients with incomplete partition type I malformation who experienced an intra-operative cerebrospinal fluid ‘gusher’ during cochlear implantation and subsequently developed meningitis due to contralateral cerebrospinal fluid leakage from a stapes footplate fistula. Detailed clinical assessments, radiological findings and surgical management are described.

In all three cases, the initial suspicion of a cerebrospinal fluid fistula was directed towards the implanted ear. However, radiological evaluation and intra-operative findings confirmed a stapes footplate fistula in the non-implanted ear. Surgical closure was achieved using temporal fascia and fibrin glue. In one case, subtotal petrosectomy was required because of persistent cerebrospinal fluid leakage.

In patients with incomplete partition type I malformations undergoing cochlear implantation, contralateral cerebrospinal fluid fistula should be considered in the differential diagnosis of post-operative meningitis.

The inner ear is a complex sensory organ with finely balanced physiology; disrupting this may cause hearing changes or vestibular symptoms. Pregnancy involves multiple significant reversible alterations in physiological state. This study reviews literature on the inner ear in pregnancy.

The review was pre-registered on the PROSPERO database CRD42023446898. Robust searches were conducted by two independent researchers according to the PRISMA 2020 guideline.

A total of 69 studies were filtered into the final analysis. Consistent evidence of subclinical hearing loss in pregnancy was identified, which resolved following childbirth. Auditory processing is affected by pregnancy. Vestibular dysfunction may contribute to pregnancy nausea. Sudden sensorineural hearing loss does not occur more frequently in pregnancy.

This review summarises evidence for reversible and irreversible changes to hearing and vestibular function in pregnancy and pregnancy-related conditions, reviewing aetiological theories and offering insight to audiovestibular physiology and explaining audiovestibular symptoms in the pregnant patient.

Temporal bone computed tomography delivers a relatively high radiation dose. Cone beam computed tomography could be a promising alternative, offering good performance with reduced radiation exposure. This study aimed to compare the irradiation during temporal bone imaging using computed tomography versus cone beam computed tomography.

We conducted a single-centre prospective study evaluating dosimetric data collected from patients undergoing temporal bone imaging via computed tomography or cone beam computed tomography. Absorbed doses (milligrays) were measured using mini-dosimeters placed on key anatomical sites: eyes, ears, lower neck and pubic region, and compared between the two imaging modalities.

CBCT significantly reduced radiation, with absorbed doses being two to six times lower than those observed with conventional computed tomography, depending on the measured sites.

Our findings align with existing literature, confirming the reduced irradiation with cone beam computed tomography in ear imaging. Further studies are warranted to evaluate image quality relative to radiation dose between the two techniques.

Cochlear implantation has transformed management of children with severe to profound hearing loss but the influence of residual hearing on outcomes remains debatable.

This ambispective study analysed 48 prelingually deaf children aged 3–8 years to evaluate auditory, speech and language outcomes following unilateral cochlear implantation. Participants were grouped based on presence of residual hearing and tracked up to 3 years post implantation.

Early improvements in auditory and speech perception were significantly higher in candidates with residual hearing but equalised by 12 months. Language outcomes initially favoured RH group with no significant difference beyond 18 months. Owing to gradual development of language, it remained below age-appropriate levels. Parental satisfaction scores were consistently better in RH group, driven by early post-implantation gains.

Residual hearing positively impacts early outcomes in cochlear implant recipients but influence diminishes over time.

The important role of the saccule is the sensing of gravity. In other words, gravity always stimulates the macula of the saccule.

The aim of this study was to clarify whether nystagmus and dizziness occur by intentional changes upon stimulation to the saccules.

The subjects were eight healthy humans. Experiment 1: Subjects were asked to maintain a supine position to check for nystagmus and dizziness. Experiment 2: Subjects were asked to tilt their heads 45º to the left in the supine position to check for nystagmus and dizziness. Experiment 3: Subjects were asked to maintain a left-ear-down 90º position to check for nystagmus and dizziness.

In all the experiments, no one revealed nystagmus and no one complained of dizziness.

Neither nystagmus nor dizziness occurs by intentional changes in the stimulation to the saccules.

Ménière’s disease is an inner-ear disorder caused by endolymphatic hydrops, characterised by recurrent episodes of vertigo, fluctuating hearing loss, and tinnitus. Ménière’s disease can be classified as ‘probable’ and ‘definite’ according to the criteria determined by the Bárány Society.

This analytical cross-sectional retrospective study included 28 Ménière’s disease patients (15 with definite Ménière’s disease and 13 with probable Ménière’s disease). Vestibular function was assessed using ocular-vestibular evoked myogenic potentials, cervical-vestibular evoked myogenic potentials and caloric test.

The results of these tests were evaluated separately for probable Ménière’s disease and definite Ménière’s disease groups and comparisons were made. Significant differences in vestibular evoked myogenic potential asymmetry rates were observed between the probable Ménière’s disease and definite Ménière’s disease groups, with the definite Ménière’s disease group exhibiting a higher rate of abnormal responses.

This suggests that vestibular evoked myogenic potentials testing may be a valuable tool in distinguishing between these two subtypes of Ménière’s disease. Further research is necessary to validate these findings and explore their implications for clinical practice.

Ménière’s disease is a chronic inner-ear disease attributed to endolymphatic hydrops. Magnetic resonance imaging with gadolinium allows visualisation of endolymphatic hydrops in vivo and may be an adjunct to diagnosis.

Thirty-eight patients suspected of having Ménière’s disease underwent T2 weighted three-dimensional fluid-attenuated inversion recovery and true inversion recovery sequence magnetic resonance imaging 4 hours post double-dose intra-venous gadolinium. Presence of endolymphatic hydrops was graded by two radiologists at 0 and 4 months. Correlation to clinical diagnosis was assessed using Fisher’s exact test.

Hydrops was identified in 88 per cent, 17 per cent and 27 per cent of patients with Definite Ménière’s, Probable Ménière’s and Undifferentiated disease, respectively. A significant correlation existed between diagnosis and presence of hydrops. Sensitivity and specificity were 88 per cent and 67 per cent, respectively. Intra- and inter-observer agreement for presence and grading of hydrops was near-perfect and substantial to near-perfect, respectively.

Magnetic resonance imaging demonstrates radiographic hydrops with significant correlation to clinical diagnosis and good intra- and inter-observer agreement.

To compare long-term impedance and functional outcomes between the round window and cochleostomy approaches in cochlear implantation patients.

Ninety prelingually deafened children who underwent unilateral cochlear implantation participated in this prospective observational study. Participants were divided into round window and cochleostomy groups. Impedance and speech perception were assessed at switch-on, and at 6, 12, and 24 months.

Impedance was similar between groups except at switch-on, where the cochleostomy group had higher basal turn impedance (2.41 vs 1.32 kΩ). At 24 months, speech outcomes were as follows: word recognition in quiet (round window 96.2 per cent, cochleostomy 95.3 per cent), word recognition in noise (round window 88.8 per cent, cochleostomy 87.4 per cent), sentence recognition (round window 78.2 per cent, cochleostomy 77.3 per cent), and vowel recognition (round window 91.2 per cent, cochleostomy 90.1 per cent).

No significant differences in impedance or speech outcomes were found between the round window and cochleostomy groups, except for higher basal-turn impedance at switch-on in the cochleostomy group, indicating more fibrosis.

Congenital hearing loss is a chronic condition which occurs worldwide. In the past, investigations focused on testing the most common genes associated with hearing loss (such as Connexin 26-related hearing loss). Targeted testing of specific genes was requested only when a particular syndrome was suspected. Recent advances have led to the development of a large gene panel which utilises next-generation sequencing to simultaneously test for pathogenic variants in many genes associated with hearing loss.

This review article aims to highlight the changes in the approach to congenital hearing loss in the context of the R67 gene panel, and how its use may increase the efficiency of the diagnosis and management of this condition.

The use of this large gene panel has revolutionised the approach to hearing loss. Uptake of this large gene panel has resulted in prompter diagnosis and therefore more appropriate clinical management.

This study evaluates the safety and utility of Eustachian tube balloon dilatation in treating Eustachian tube dysfunction symptoms in adults without middle-ear disease.

A prospective cohort study was performed. Adults with dilatory Eustachian tube dysfunction symptoms and no middle-ear disease underwent Eustachian tube balloon dilatation. A clinical assessment including tympanometry, pure tone audiometry, otoscopy, ability to Valsalva, and Eustachian Tube Dysfunction Questionnaire-7 was performed pre-operatively and repeated during a 12-month follow-up period.

Fifteen participants were enrolled. The mean pre-operative Eustachian Tube Dysfunction Questionnaire-7 score of 4.6 reduced to 2.5 at six weeks (P < 0.01), 3.0 at six months (P = 0.02) and 2.6 at 12 months (P < 0.01) post-operatively. All patients without evidence of negative middle-ear pressure had Eustachian Tube Dysfunction Questionnaire-7 score improvements. There were no post-operative complications.

Eustachian tube balloon dilatation is safe and effective at treating Eustachian tube dysfunction in patients with no middle-ear disease or evidence of negative middle-ear pressure.

This study aimed to evaluate clinical characteristics, treatments and outcomes of paediatric temporal bone fractures at our institute.

A retrospective study of paediatric skull fractures confirmed by imaging from January 2010 to December 2022. Data on demographics, clinical presentations, injury mechanisms and complications were analysed, and fractures were categorised into otic capsule sparing (OCS) and violating (OCV).

Of 369 skull fracture cases, 88 (24 per cent) involved temporal bones, predominantly caused by falls and vehicle accidents. Common symptoms were loss of consciousness, hematoma, and hemotympanum, with complications like facial nerve injury and cerebrospinal fluid leaks in 3.4 per cent of cases. OCV fractures led to more severe complications, including hearing loss. Audiology showed 65 per cent without hearing impairment, while others had various degrees of loss.

Paediatric temporal bone fractures, particularly OCV types, pose significant challenges. Early detection and thorough management are vital, underscoring the need for consistent data collection and regular audiometric monitoring.

Patients presenting to the emergency department with acute vertigo pose a diagnostic challenge. While ‘benign’ peripheral vestibulopathy is the most common cause, the possibility of a posterior circulation stroke is paradoxically the most feared and missed diagnosis in the emergency department.

This review will attempt to cover the significant advances in the ability to diagnose acute vertigo that have occurred in the last two decades. The review discusses the role of neurological examinations, imaging and specific oculomotor examinations. The review then discusses the relative attributes of the Head Impulse-Nystagmus-Test of Skew plus hearing (‘HINTS+’) examination, the timing, triggers and targeted bedside eye examinations (‘TiTrATE’), the associated symptoms, timing and triggers, examination signs and testing (‘ATTEST’) algorithm, and the spontaneous nystagmus, direction, head impulse testing and standing (‘STANDING’) algorithm. The most recent technological advancements in video-oculography guided care are discussed, as well as other potential advances for clinicians to look out for.

Balance dysfunction and vestibular conditions are major problems requiring significant resources. There is significant national and international variation in management pathways for such patients.

This paper outlines a collaborative project run by the ENT department and two vestibular rehabilitation trained physiotherapists to establish a clinic to manage patients referred to ENT with vestibular and/or balance complaints. As part of a six-month pilot, two physiotherapy-led balance clinics were provided per week.

A total of 159 new patients were seen, with only 15 needing ENT consultant input. This led to the successful creation of substantive posts; the clinic has seen 698 patients in its first two years.

Patient outcomes and experience have been positive, and accompanied by reduced waiting and in-service times. The authors discuss some of the pitfalls, challenges and opportunities of developing this type of clinic.

This pilot study aimed to evaluate a training programme for primary care physiotherapists focused on the assessment and management of benign paroxysmal positional vertigo.

A six-month training programme and toolkit utilising the revised Standards for Quality Improvement Reporting Excellence (‘SQUIRE 2.0’) guidelines was developed to facilitate the learning of new knowledge and skills in the assessment and management of benign paroxysmal positional vertigo following Gagne's model of instructional design. A pre- and post-training knowledge and confidence questionnaire evaluated the impact of the training programme.

Eleven participants started the training programme and five completed it. On average, knowledge increased by 54 per cent (range, 41–95 per cent) and confidence increased by 45 per cent (range, 31–76 per cent). A 73 per cent improvement in practical skills acquisition was demonstrated after the initial training session.

A structured approach to learning demonstrates improvements in knowledge, skills and confidence of physiotherapists in the evidence-based management of benign paroxysmal positional vertigo.

To examine the newly established role of a primary contact physiotherapist in an ENT clinic, in an Australian cohort and context, over two phases of development.

A retrospective cohort study was conducted with data collected from a medical record audit. Over the study duration, the primary contact physiotherapist completed initial appointments with patients; follow-up appointments were subsequently conducted by medical staff.

There was a 46 per cent reduction in patients with suggested vestibulopathy requiring an ENT medical review. This reduction could hypothetically increase to 71 per cent with follow-up primary contact physiotherapist appointments. Improvements in the service delivery model and a primary contact physiotherapist arranging diagnostic assessments could improve waitlist times and facilitate better utilisation of medical staff time.

The primary contact physiotherapist can help in the management of patients with suspected vestibulopathy on an ENT waitlist. This is achieved through: a reduction of patients requiring ENT review, improvements to waitlist time and improved utilisation of medical specialists’ time.

Persistent postural-perceptual dizziness classifies patients with chronic dizziness, often triggered by an acute episode of vestibular dysfunction or threat to balance. Unsteadiness and spatial disorientation vary in intensity but persist for over three months, exacerbated by complex visual environments.

Literature suggests diagnosis relies on a clinical history of persistent subjective dizziness and normal vestibular and neurological examination findings. Behavioural diagnostic biomarkers have been proposed, to facilitate diagnosis.

Research has focused on understanding the neural mechanisms that underpin this perceptual disorder, with imaging data supporting altered connectivity between neural brain networks that process vision, motion and emotion. Behavioural research identified the perceptual and motor responses to a heightened perception of imbalance.

Management utilises head and body motion detection, and downregulation of visual motion excitability, reducing postural hypervigilance and anxiety. Combinations of physical and cognitive therapies, with antidepressant medications, help if the condition is associated with mood disorder.

Differential diagnosis of acute vertigo syndrome is challenging given the similarities between clinical presentations of posterior circulation stroke and peripheral vestibular dysfunction. The Head Impulse, Nystagmus, Test of Skew (‘HINTS’) assessment is a clinical bedside test used to aid diagnosis.

Comprehensive training on use of the Head Impulse, Nystagmus, Test of Skew assessment was provided to one stroke consultant, and the effectiveness of the test in that setting was assessed. Further education was completed with more members of the stroke and emergency department multi-disciplinary team. Quality improvement measures including magnetic resonance imaging use and bed utilisation were explored.

Following training of one stroke consultant, the Head Impulse, Nystagmus, Test of Skew assessment was found to be a feasible, accurate bedside test within this acute stroke service. Further training for the multi-disciplinary team was completed, but outcome measures were not explored because of the coronavirus disease 2019 pandemic and maternity leave.

There is a role for trained members of the multi-disciplinary team to successfully use the Head Impulse, Nystagmus, Test of Skew assessment in hyperacute stroke settings, to aid diagnosis in acute vertigo syndrome.

Driving capacity is affected by vestibular disorders and the medications used to treat them. Driving is not considered during medical consultations, with 92 per cent of patients attending a centre for dizziness not discussing it with the doctor.

To investigate if medical record prompts facilitate dizziness and driving conversations in ENT balance clinics.

A questionnaire was designed to reflect the current standards of practice and advice given regarding driving and dizziness during balance clinic consultations.

Medical record prompts facilitated the improved frequency and recording of shared decision-making conversations about driving and dizziness in 98 per cent of consultations.

This study highlights the benefits of medical record prompts for documented and accurate shared decision-making conversations surrounding dizziness, vertigo, vestibular conditions and driving. This potentially improves safety for all road users, and protects the patient and clinician in the event of road traffic accidents and medico-legal investigations.